{"entities":{"Q43558":{"pageid":33926,"ns":120,"title":"Item:Q43558","lastrevid":155923,"modified":"2026-08-13T10:37:52Z","type":"item","id":"Q43558","labels":{"mul":{"language":"mul","value":"FB51.4"},"pt-br":{"language":"pt-br","value":"Fibrose retroperitoneal"},"en":{"language":"en","value":"Retroperitoneal fibrosis"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Fibrose retroperitoneal (FRP) \u00e9 uma doen\u00e7a caracterizada pela forma\u00e7\u00e3o de extensa prolifera\u00e7\u00e3o de tecido fibroso no retroperit\u00f4nio, resultando em encarceramento e obstru\u00e7\u00e3o de estruturas retroperitoneais, particularmente os ureteres. A FRP pode ser classificada em prim\u00e1ria (idiop\u00e1tica), o que significa que sua causa n\u00e3o \u00e9 conhecida, ou secund\u00e1ria. No entanto, sua associa\u00e7\u00e3o com v\u00e1rias condi\u00e7\u00f5es imunomediadas e sua resposta ao tratamento imunossupressor t\u00eam levado \u00e1 especula\u00e7\u00e3o de etiologia autoimune para a FRP idiop\u00e1tica. Um ter\u00e7o dos casos s\u00e3o secund\u00e1rios a neoplasias malignas, medicamentos, traumatismo e algumas infec\u00e7\u00f5es."},"en":{"language":"en","value":"Retroperitoneal fibrosis (RPF) is a disease characterised by the development of extensive proliferation of fibrous tissue in the retroperitoneum, resulting in entrapment and obstruction of retroperitoneal structures, notably the ureters. RPF can be classified as primary (idiopathic) meaning that the cause is not known or secondary. But its association with various immune-related conditions and response to immunosuppression have led to speculation regarding an autoimmune aetiology of idiopathic RPF. One-third of the cases are secondary to malignancy, medication, trauma, or certain infections."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"d5c03b1717b713dc8dee0aa8cb4f9c41ee81c96c","datavalue":{"value":"https://id.who.int/icd/entity/967295607","type":"string"},"datatype":"url"},"type":"statement","id":"Q43558$DC9F93D9-28AC-47F2-8BFB-25A1F9D2D0D0","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"7ec916b2b957af0eeec35b3c26099fb46a3c0076","datavalue":{"value":"CID11:FB51.4","type":"string"},"datatype":"string"},"type":"statement","id":"Q43558$545D788E-1FBB-49D9-90D7-047204ACFD94","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"62b5ac0510deb649c7640fec1a49a9b5f28b052c","datavalue":{"value":"dki-india-FB51.4","type":"string"},"datatype":"string"},"type":"statement","id":"Q43558$E5C6E918-BFCB-4CA1-95E1-A2830C58198D","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q43558$4B57C524-88A4-457A-93A6-8ACB2E9361D4","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q43558$6FD1E3DC-0DAF-4608-9F88-51DCAA85F2A2","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q43558$F8EBFACF-F929-45C2-94A2-7EC563B2ADCD","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"f22cf25a9dd0401dff43ed7c515ce0d2effba0de","datavalue":{"value":{"entity-type":"item","numeric-id":43557,"id":"Q43557"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q43558$E43A2436-F598-4D62-A9B7-8439F86C1728","rank":"normal"}]},"sitelinks":{}}}}