{"entities":{"Q42980":{"pageid":33348,"ns":120,"title":"Item:Q42980","lastrevid":150941,"modified":"2026-08-13T09:45:41Z","type":"item","id":"Q42980","labels":{"mul":{"language":"mul","value":"CB40.0"},"pt-br":{"language":"pt-br","value":"Discinesia ciliar"},"en":{"language":"en","value":"Ciliary dyskinesia"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Fun\u00e7\u00e3o defeituosa dos c\u00edlios revestindo o trato respirat\u00f3rio (inferior e superior, seios, tuba auditiva, orelha m\u00e9dia) resultando em transporte mucociliar alterado e se manifestando como como infec\u00e7\u00e3o recorrente de vias a\u00e9reas superiores e inferiores, tosse cr\u00f4nica produtiva, rinossinusite cr\u00f4nica ou otite m\u00e9dia persistente. As forma adquiridas resultam de les\u00e3o do trato respirat\u00f3rio associada principalmente a infec\u00e7\u00f5es como bronquiolites ou doen\u00e7a pulmonar obstrutiva cr\u00f4nica. As raras formas prim\u00e1rias s\u00e3o herdadas como transtorno autoss\u00f4mico recessivo que se apresenta precocemente na vida e tipicamente progridem para bronquiectasias; podem estar associadas a infertilidade no homem e na mulher, devido a mobilidade anormal dos espermatozoides ou da fun\u00e7\u00e3o alterada das tubas uterinas, respectivamente."},"en":{"language":"en","value":"Defective function of the cilia lining the respiratory tract (lower and upper, sinuses, Eustachian tube, middle ear) resulting in altered mucociliary transport and manifesting as recurrent upper and lower respiratory infection, chronic productive cough, chronic rhinosinusitis or persistent otitis media. Acquired forms result from respiratory tract injury associated especially with respiratory infections such as bronchiolitis or chronic obstructive pulmonary disease. The rare primary forms are inherited as autosomal recessive disorders presenting early in life and typically progressing to bronchiectasis; they may be associated with infertility in men and women due to abnormal sperm motility or fallopian tube function respectively."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"c444c2be66d0fdfec62db7a100cd56da9d4fce50","datavalue":{"value":"https://id.who.int/icd/entity/955573234","type":"string"},"datatype":"url"},"type":"statement","id":"Q42980$AFFE31C7-A015-4BF3-87FD-79C16CC19471","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"fab23f081727f1b5c7caada43f5e83d136753853","datavalue":{"value":"CID11:CB40.0","type":"string"},"datatype":"string"},"type":"statement","id":"Q42980$4141AEA2-7F08-442B-9F8B-93AE69EF1882","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"b5783e94ff8bc19d0f7806da3c62d884aef0da40","datavalue":{"value":"dki-india-CB40.0","type":"string"},"datatype":"string"},"type":"statement","id":"Q42980$24FFF067-2DB8-48B9-9BEC-E17C37DBEAFE","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q42980$495FBEA5-D562-47D7-9C27-F915B245F690","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q42980$7BB37BB0-5A0E-48D6-8265-52267DB9E69C","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q42980$DA3D6063-571D-45E9-B04F-0CD7C7310B80","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"b32429645ba47fe73df25ffaca0546565524a11c","datavalue":{"value":{"entity-type":"item","numeric-id":42979,"id":"Q42979"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q42980$2C296242-0C45-4F7C-8765-FF50EFDF833E","rank":"normal"}]},"sitelinks":{}}}}