{"entities":{"Q42953":{"pageid":33321,"ns":120,"title":"Item:Q42953","lastrevid":150712,"modified":"2026-08-13T09:43:28Z","type":"item","id":"Q42953","labels":{"mul":{"language":"mul","value":"CB07.0"},"pt-br":{"language":"pt-br","value":"Linfangioleiomiomatose associada a complexo de esclerose tuberosa"},"en":{"language":"en","value":"Lymphangioleiomyomatosis associated with tuberous sclerosis complex"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Doen\u00e7a pulmonar rara que resulta na prolifera\u00e7\u00e3o de crescimento desordenado de m\u00fasculo liso (leiomioma) nos pulm\u00f5es inteiros, nos bronqu\u00edolos, septos alveolares espa\u00e7os perivasculares e linf\u00e1ticos, o que resulta na obstru\u00e7\u00e3o das pequenas vias a\u00e9reas (levando \u00e0 forma\u00e7\u00e3o de cistos pulmonares e pneumot\u00f3rax) e dos linf\u00e1ticos (levando a derrame pleural quiloso). Este diagn\u00f3stico est\u00e1 associado a uma doen\u00e7a multissist\u00eamica gen\u00e9tica rara que causa o crescimento de tumores n\u00e3o malignos no c\u00e9rebro e em outros \u00f3rg\u00e3os vitais como rins, cora\u00e7\u00e3o, olhos, pulm\u00f5es e pele."},"en":{"language":"en","value":"This is a rare lung disease that results in a proliferation of disorderly smooth muscle growth (leiomyoma) throughout the lungs, in the bronchioles, alveolar septa, perivascular spaces, and lymphatics, resulting in the obstruction of small airways (leading to pulmonary cyst formation and pneumothorax) and lymphatics (leading to chylous pleural effusion). This diagnosis is associated with a rare multi-system genetic disease that causes non-malignant tumours to grow in the brain and on other vital organs such as the kidneys, heart, eyes, lungs, and skin."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"498c9f3bc9db8f6bd7e6116845fa6fa67ee0dbc9","datavalue":{"value":"https://id.who.int/icd/entity/1746892004","type":"string"},"datatype":"url"},"type":"statement","id":"Q42953$99225EA3-CC7C-445B-A1FB-778EC6714729","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"ea6526047fd0f72dc7bff5179286ffbd515523e4","datavalue":{"value":"CID11:CB07.0","type":"string"},"datatype":"string"},"type":"statement","id":"Q42953$61221DE3-39D5-4EF3-A4EB-897E397273BC","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"106807c06197fc64f63e5a885e67c7239a396348","datavalue":{"value":"dki-india-CB07.0","type":"string"},"datatype":"string"},"type":"statement","id":"Q42953$D3E736C2-B59E-46E0-86A3-E01A008A31DD","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q42953$6C9CED36-E2B4-4C2E-BA38-0ED239CD982F","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q42953$EA6EEADD-DD6E-4261-BC17-3436DC3E2EB3","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q42953$F6142D88-C143-4C6E-AF10-5F64608AA5A0","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"650f08651bdaf59448369e90a98ac51615f4d99e","datavalue":{"value":{"entity-type":"item","numeric-id":18778,"id":"Q18778"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q42953$B2FECC9D-C878-4ED8-9F52-449657FA82E0","rank":"normal"}]},"sitelinks":{}}}}