{"entities":{"Q42853":{"pageid":33221,"ns":120,"title":"Item:Q42853","lastrevid":149856,"modified":"2026-08-13T09:34:44Z","type":"item","id":"Q42853","labels":{"mul":{"language":"mul","value":"CA26.1"},"pt-br":{"language":"pt-br","value":"Panbronquiolite difusa"},"en":{"language":"en","value":"Diffuse panbronchiolitis"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Panbronquiolite difusa (PBD) \u00e9 uma doen\u00e7a inflamat\u00f3ria idiop\u00e1tica que afeta principalmente os bronqu\u00edolos respirat\u00f3rios, causando um transtorno respirat\u00f3rio obstrutivo grave progressivo de natureza supurativa. O in\u00edcio ocorre entre a segunda e quinta d\u00e9cadas da vida, e se manifesta com tosse cr\u00f4nica, dispneia ao esfor\u00e7o e produ\u00e7\u00e3o de escarro. A maioria dos pacientes apresenta tamb\u00e9m sinusite cr\u00f4nica. Se n\u00e3o tratada, a PBD progride para bronquiectasias, insufici\u00eancia respirat\u00f3ria e morte. Melhora significativa do progn\u00f3stico foi relatada gra\u00e7as ao uso de antibi\u00f3ticos macrol\u00eddeos, cujo efeito \u00e9 atribu\u00eddo a uma a\u00e7\u00e3o anti-inflamat\u00f3ria e autorreguladora."},"en":{"language":"en","value":"Diffuse panbronchiolitis (DPB) is an idiopathic inflammatory disease principally affecting the respiratory bronchioles, causing a progressive suppurative and severe obstructive respiratory disorder. Onset occurs in the second to fifth decade of life and manifests by chronic cough, exertional dyspnoea, and sputum production. Most patients also have chronic paranasal sinusitis. If left untreated, DPB progresses to bronchiectasis, respiratory failure and death. A significant improvement in the prognosis has been reported thanks to the use of long-term therapy with macrolide antibiotics, the effect of which is attributed to an anti-inflammatory and immunoregulatory action."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"71e15eeeedf23927bf95b436461d5de6f5694e18","datavalue":{"value":"https://id.who.int/icd/entity/291357751","type":"string"},"datatype":"url"},"type":"statement","id":"Q42853$0F2811A8-AFCB-44BD-B35C-523C1D7D0B92","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"2ac35f642949674420fe11dba46819363d14cf35","datavalue":{"value":"CID11:CA26.1","type":"string"},"datatype":"string"},"type":"statement","id":"Q42853$A7262AF6-780E-4CB2-9A11-197439975541","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"e87ddd8570cfe2b5fc2e54d8f89009b8b1351868","datavalue":{"value":"dki-india-CA26.1","type":"string"},"datatype":"string"},"type":"statement","id":"Q42853$7C0E5E00-097E-4CD8-9302-5B5E2B5A6474","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q42853$EAE79C41-CC10-4000-BF77-BF579D7E5719","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q42853$C62A88F7-3B7D-4555-9657-9AC56B0419DC","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q42853$94F87168-2479-4FEE-9C02-3688EF344EA1","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"6ec9f95c15ad2399599f0a2fef095719973de9c9","datavalue":{"value":{"entity-type":"item","numeric-id":18711,"id":"Q18711"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q42853$E27C98CE-FCFE-4BB1-8269-E1F0303767A0","rank":"normal"}]},"sitelinks":{}}}}