{"entities":{"Q41390":{"pageid":31758,"ns":120,"title":"Item:Q41390","lastrevid":137742,"modified":"2026-08-13T07:32:42Z","type":"item","id":"Q41390","labels":{"mul":{"language":"mul","value":"8C71.0"},"pt-br":{"language":"pt-br","value":"Distrofia miot\u00f4nica"},"en":{"language":"en","value":"Myotonic dystrophy"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Distrofia miot\u00f4nica \u00e9 um grupo de transtornos musculares heredit\u00e1rios. \u00c9 a forma mais comum de distrofia muscular que come\u00e7a na idade adulta. A distrofia miot\u00f4nica \u00e9 caracterizada por atrofia e fraqueza musculares progressivas e contra\u00e7\u00f5es musculares prolongadas (miotonia) que n\u00e3o s\u00e3o capazes de relaxar ap\u00f3s o uso. Outros sinais e sintomas de distrofia miot\u00f4nica incluem fala arrastada ou bloqueio tempor\u00e1rio da mand\u00edbula, catarata e defeitos de condu\u00e7\u00e3o card\u00edaca. Em homens afetados, altera\u00e7\u00f5es hormonais podem levar a calv\u00edcie precoce e infertilidade. A gravidade cl\u00ednica varia amplamente entre os pacientes afetados, mesmo entre membros da mesma fam\u00edlia."},"en":{"language":"en","value":"Myotonic dystrophy is a group of inherited muscular disorders. It is the most common form of muscular dystrophy that begins in adulthood. Myotonic dystrophy is characterised by progressive muscle wasting and weakness, and prolonged muscle contractions (myotonia) that are not able to relax after use. Other signs and symptoms of myotonic dystrophy include slurred speech or temporary locking of their jaw, cataracts and cardiac conduction defects. In affected men, hormonal changes may lead to early balding and infertility. The clinical severity varies widely among affected patients, even among members of the same family."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"a7df5701db646f86e3993c1aecace7758fc9d4ce","datavalue":{"value":"https://id.who.int/icd/entity/192087511","type":"string"},"datatype":"url"},"type":"statement","id":"Q41390$A9F33B02-2FDB-4395-8078-119F5C344EF2","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"5d87b0d3fa5f9f47c17cce3caf12c724f007413d","datavalue":{"value":"CID11:8C71.0","type":"string"},"datatype":"string"},"type":"statement","id":"Q41390$DE29E177-3467-48DD-AAA3-9E579802F40E","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"4dde09fc5ba481042277ad421ff2ccb73e842a63","datavalue":{"value":"dki-india-8C71.0","type":"string"},"datatype":"string"},"type":"statement","id":"Q41390$397FB050-B383-4F39-B6BC-AE5AC2AC7EBE","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q41390$CFA25372-F8B2-43EC-97CC-1A0F28F5BC7F","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q41390$A5F69F9E-74B4-4E91-9FA9-2DB6D45E5AD3","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q41390$1EFC7141-8D19-4FC4-B276-93068D3E81F4","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"e1b713d1aee9878f927228efdab4c66c06611ce7","datavalue":{"value":{"entity-type":"item","numeric-id":17303,"id":"Q17303"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q41390$C78B58F7-26A3-48A0-842B-6F3F8B395E4F","rank":"normal"}]},"sitelinks":{}}}}