{"entities":{"Q41271":{"pageid":31639,"ns":120,"title":"Item:Q41271","lastrevid":136707,"modified":"2026-08-13T07:22:44Z","type":"item","id":"Q41271","labels":{"mul":{"language":"mul","value":"7A42.3"},"pt-br":{"language":"pt-br","value":"Hipoventila\u00e7\u00e3o alveolar central idiop\u00e1tica"},"en":{"language":"en","value":"Idiopathic central alveolar hypoventilation"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Hipoventila\u00e7\u00e3o alveolar central idiop\u00e1tica \u00e9 definida como a presen\u00e7a de ventila\u00e7\u00e3o alveolar reduzida resultando em hipercapnia e hipoxemia relacionadas ao sono em indiv\u00edduos com propriedades mec\u00e2nicas do pulm\u00e3o e da bomba respirat\u00f3ria normais presumidas. Hipoventila\u00e7\u00e3o cr\u00f4nica durante o sono existe sem qualquer comprometimento prontamente identific\u00e1vel da respira\u00e7\u00e3o, tal como condi\u00e7\u00f5es de vias a\u00e9reas ou par\u00eanquima pulmonares, anormalidades neurol\u00f3gicas, neuromusculares ou de parede tor\u00e1cica, obesidade grave, outro transtorno respirat\u00f3rio relacionado ao sono, ou uso de medicamentos ou subst\u00e2ncias depressivos respirat\u00f3rios. Tanto a hipoventila\u00e7\u00e3o diurna como a noturna s\u00e3o consideradas como primariamente devidas a quimiorresponsividade embotada ao di\u00f3xido de carbono (CO2) e ao oxig\u00eanio (O2). Os pacientes podem se queixar de cefaleia matinal, fadiga, decl\u00ednio neurocognitivo e dist\u00farbio do sono, ou podem ser completamente assintom\u00e1ticos._x000D_ _x000D_ Nota: Um diagn\u00f3stico definitivo requer a evid\u00eancia objetiva baseada em polissonografia com monitoriza\u00e7\u00e3o do di\u00f3xido de carbono (CO2) por medidas arterial, tidal final ou transcut\u00e2nea."},"en":{"language":"en","value":"Idiopathic central alveolar hypoventilation is defined as the presence of decreased alveolar ventilation resulting in sleep related hypercapnia and hypoxemia in individuals with presumed normal mechanical properties of the lung and respiratory pump. Chronic hypoventilation during sleep exists without any readily identifiable impairments of respiration, such as pulmonary airway or parenchymal conditions, neurologic, neuromuscular or chest wall abnormalities, severe obesity, other sleep related breathing disorder, or use of respiratory depressant medications or substances. Diurnal as well as nocturnal hypoventilation is believed to be due primarily to blunted chemoresponsiveness to carbon dioxide (CO2) and oxygen (O2). Patients may complain of morning headaches, fatigue, neurocognitive decline and sleep disturbance, or may be entirely asymptomatic. Note: A definitive diagnosis requires objective evidence based on polysomnography with carbon dioxide (CO2) monitoring (by arterial, end-tidal or transcutaneous measures)."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"bf3ec5c16bbc9850951ec586e1169584c5a49e0b","datavalue":{"value":"https://id.who.int/icd/entity/1024837047","type":"string"},"datatype":"url"},"type":"statement","id":"Q41271$9D930CD8-CEAB-4E0C-A5AE-49CD70D04787","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"5d4dac02040f2feae9ebf9c0ba50b852bb83decb","datavalue":{"value":"CID11:7A42.3","type":"string"},"datatype":"string"},"type":"statement","id":"Q41271$CBAE303C-A4D7-480A-A7D6-CCF711B19F41","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"5129cc264c9df5e1d4ea2e11b836ade519cf3fe1","datavalue":{"value":"dki-india-7A42.3","type":"string"},"datatype":"string"},"type":"statement","id":"Q41271$A8D57859-F011-4458-BF00-115165578DA2","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q41271$34092ACD-77F5-4AAE-8428-586346780584","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q41271$7CC8C34E-877A-43C3-A895-A28A08629252","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q41271$85E358DF-4E99-44B7-9576-0EF1E4DA8A32","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"4edf39454276e1f01ecf2a3245450e8c7bcb733c","datavalue":{"value":{"entity-type":"item","numeric-id":17084,"id":"Q17084"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q41271$60A88C7B-443D-415A-8647-666E960CD214","rank":"normal"}]},"sitelinks":{}}}}