{"entities":{"Q41049":{"pageid":31417,"ns":120,"title":"Item:Q41049","lastrevid":134915,"modified":"2026-08-13T07:06:15Z","type":"item","id":"Q41049","labels":{"mul":{"language":"mul","value":"8B60.4"},"pt-br":{"language":"pt-br","value":"Esclerose lateral prim\u00e1ria"},"en":{"language":"en","value":"Primary lateral sclerosis"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Esclerose lateral prim\u00e1ria (ELP) \u00e9 uma variante rara da doen\u00e7a do neur\u00f4nio motor que se apresenta com sinais de NMS lentamente progressivos, como marcha esp\u00e1stica, espasmos bruscos intensos dos tend\u00f5es e respostas extensoras plantares. O in\u00edcio \u00e9 mais comumente com paraparesia esp\u00e1stica, mas os pacientes tipicamente evoluem para desenvolver envolvimento bulbar e de membros superiores. O aspecto caracter\u00edstico da ELP \u00e9 a completa aus\u00eancia de envolvimento do envolvimento do neur\u00f4nio motor inferior. Quando os sinais de LMN se desenvolvem durante o curso da doen\u00e7a, o diagn\u00f3stico muda para ELA, e eles s\u00e3o considerados um espectro do mesmo transtorno."},"en":{"language":"en","value":"Primary lateral sclerosis (PLS) is a rare motor neuron disease variant which presents with slowly progressive UMN signs, such as spastic gait, brisk deep tendon jerks, and extensor plantar responses. Onset is most commonly with spastic paraparesis, but patients typically progress to develop upper limb and bulbar involvement. The characteristic feature of PLS is the complete absence of involvement of lower motor neuron involvement. When LMN signs develop during the course of the disease, the diagnosis will change to ALS, and they are considered a spectrum of the same disorder."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"0f59ed0e433e4aa3a8829a8c7953bee59edc45cf","datavalue":{"value":"https://id.who.int/icd/entity/1686688462","type":"string"},"datatype":"url"},"type":"statement","id":"Q41049$7A1EE355-5A22-4747-A9D5-1EF178791420","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"a8837df079210129ab0b481392f9cb87e3be83ff","datavalue":{"value":"CID11:8B60.4","type":"string"},"datatype":"string"},"type":"statement","id":"Q41049$9F993FF3-FBA9-45A6-BBEF-9235095C8EE0","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"223154467135de439324295c6f93c2d9932a5a8d","datavalue":{"value":"dki-india-8B60.4","type":"string"},"datatype":"string"},"type":"statement","id":"Q41049$A4B6FE91-FF7F-4710-B936-D6B98E14A149","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q41049$3D4A6949-D1BA-4CDB-AB66-6E7F92D02CE3","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q41049$AE3F6246-1078-481E-A1A4-C0059DACBB15","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q41049$666E63D9-ED09-4F4B-9080-C5087D9E0BA1","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"ea31a01f219e449243632e6aea5d14e92c40b2c6","datavalue":{"value":{"entity-type":"item","numeric-id":16832,"id":"Q16832"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q41049$FB477534-2E0D-460B-9440-1956D38FC199","rank":"normal"}]},"sitelinks":{}}}}