{"entities":{"Q40248":{"pageid":30616,"ns":120,"title":"Item:Q40248","lastrevid":127888,"modified":"2026-08-13T05:58:47Z","type":"item","id":"Q40248","labels":{"mul":{"language":"mul","value":"6D85.5"},"pt-br":{"language":"pt-br","value":"Dem\u00eancia devida a doen\u00e7a pri\u00f4nica"},"en":{"language":"en","value":"Dementia due to prion disease"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Dem\u00eancia devida a doen\u00e7a pri\u00f4nica \u00e9 uma doen\u00e7a neurodegenerativa prim\u00e1ria causada por um grupo de encefalopatias espongiformes resultantes do ac\u00famulo anormal de prote\u00ednas pri\u00f4nicas anormais no c\u00e9rebro. Podem ser espor\u00e1dicas, gen\u00e9ticas (causadas por muta\u00e7\u00f5es no gene da prote\u00edna pri\u00f4nica), ou transmiss\u00edveis (adquiridas de um indiv\u00edduo infectado). O in\u00edcio \u00e9 insidioso e h\u00e1 uma r\u00e1pida progress\u00e3o dos sintomas e comprometimento caracterizado por d\u00e9ficits cognitivos, ataxia, e sintomas motores (mioclonia, coreia, ou distonia). O diagn\u00f3stico tipicamente \u00e9 feito baseado em estudos de imagem cerebral, presen\u00e7a de prote\u00ednas caracter\u00edsticas no l\u00edquor, EEG, ou testes gen\u00e9ticos."},"en":{"language":"en","value":"Dementia due to prion disease is a primary neurodegenerative disease caused by a group of spongiform encephalopathies resulting from abnormal prion protein accumulation in the brain. These can be sporadic, genetic (caused by mutations in the prion-protein gene), or transmissible (acquired from an infected individual). Onset is insidious and there is a rapid progression of symptoms and impairment characterised by cognitive deficits, ataxia, and motor symptoms (myoclonus, chorea, or dystonia). Diagnosis is typically made on the basis of brain imaging studies, presence of characteristic proteins in spinal fluid, EEG, or genetic testing."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"8682da3628721ab1dd4a833eb598bc2053caecae","datavalue":{"value":"https://id.who.int/icd/entity/1206955889","type":"string"},"datatype":"url"},"type":"statement","id":"Q40248$3DFC1946-D632-45F5-BC16-DCF0D83F8670","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"77ca456f6f4e7169c7e1e9e4c88cd75fd26a4d8d","datavalue":{"value":"CID11:6D85.5","type":"string"},"datatype":"string"},"type":"statement","id":"Q40248$35339D03-7355-4393-86F9-841EAFFD570D","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"84854c3bfa1ac2d6b224478e40c039fd13068137","datavalue":{"value":"dki-india-6D85.5","type":"string"},"datatype":"string"},"type":"statement","id":"Q40248$B231947F-B66D-4655-A212-938EEA1E9EB7","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q40248$2FC40D33-4A89-4D98-AB62-34A648D4FA3C","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q40248$C1E4AC5F-0083-43BC-84F1-BE0FCE76890A","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q40248$9823BF95-0BF3-435E-9F6A-EFE8ADE555C1","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"5b7188ef12e5625cbd9f86a2f2b187883ac195e5","datavalue":{"value":{"entity-type":"item","numeric-id":15838,"id":"Q15838"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q40248$C3ED7CA5-3799-4C8F-9E2D-43C28CF97355","rank":"normal"}]},"sitelinks":{}}}}