@prefix rdf: <http://www.w3.org/1999/02/22-rdf-syntax-ns#> .
@prefix xsd: <http://www.w3.org/2001/XMLSchema#> .
@prefix rdfs: <http://www.w3.org/2000/01/rdf-schema#> .
@prefix owl: <http://www.w3.org/2002/07/owl#> .
@prefix wikibase: <http://wikiba.se/ontology#> .
@prefix skos: <http://www.w3.org/2004/02/skos/core#> .
@prefix schema: <http://schema.org/> .
@prefix cc: <http://creativecommons.org/ns#> .
@prefix geo: <http://www.opengis.net/ont/geosparql#> .
@prefix prov: <http://www.w3.org/ns/prov#> .
@prefix wd: <https://determinar.ia.br/entity/> .
@prefix data: <https://determinar.ia.br/wiki/Special:EntityData/> .
@prefix wds: <https://determinar.ia.br/entity/statement/> .
@prefix wdref: <https://determinar.ia.br/reference/> .
@prefix wdv: <https://determinar.ia.br/value/> .
@prefix wdt: <https://determinar.ia.br/prop/direct/> .
@prefix wdtn: <https://determinar.ia.br/prop/direct-normalized/> .
@prefix p: <https://determinar.ia.br/prop/> .
@prefix ps: <https://determinar.ia.br/prop/statement/> .
@prefix psv: <https://determinar.ia.br/prop/statement/value/> .
@prefix psn: <https://determinar.ia.br/prop/statement/value-normalized/> .
@prefix pq: <https://determinar.ia.br/prop/qualifier/> .
@prefix pqv: <https://determinar.ia.br/prop/qualifier/value/> .
@prefix pqn: <https://determinar.ia.br/prop/qualifier/value-normalized/> .
@prefix pr: <https://determinar.ia.br/prop/reference/> .
@prefix prv: <https://determinar.ia.br/prop/reference/value/> .
@prefix prn: <https://determinar.ia.br/prop/reference/value-normalized/> .
@prefix wdno: <https://determinar.ia.br/prop/novalue/> .

data:Q40066 a schema:Dataset ;
	schema:about wd:Q40066 ;
	cc:license <http://creativecommons.org/publicdomain/zero/1.0/> ;
	schema:softwareVersion "1.0.0" ;
	schema:version "126293"^^xsd:integer ;
	schema:dateModified "2026-08-13T05:43:46Z"^^xsd:dateTime ;
	wikibase:statements "7"^^xsd:integer ;
	wikibase:sitelinks "0"^^xsd:integer ;
	wikibase:identifiers "0"^^xsd:integer .

wd:Q40066 a wikibase:Item ;
	wdt:P68 <https://id.who.int/icd/entity/1295299670> ;
	wdt:P67 "CID11:5C52.11" ;
	wdt:P70 "dki-india-5C52.11" ;
	wdt:P86 "Concluído" ;
	wdt:P78 <https://pauloleads.com.br/cases-publicos/> ;
	wdt:P80 "2026-08-13T00:00:00Z"^^xsd:dateTime ;
	wdt:P89 wd:Q15613 ;
	p:P68 wds:Q40066-EB766D3D-8B20-4309-89F1-B078147ABA4A .

wds:Q40066-EB766D3D-8B20-4309-89F1-B078147ABA4A a wikibase:Statement,
		wikibase:BestRank ;
	wikibase:rank wikibase:NormalRank ;
	ps:P68 <https://id.who.int/icd/entity/1295299670> .

wd:Q40066 p:P67 wds:Q40066-0B59524E-2AF6-4A1B-B5D1-F6A25895DCCE .

wds:Q40066-0B59524E-2AF6-4A1B-B5D1-F6A25895DCCE a wikibase:Statement,
		wikibase:BestRank ;
	wikibase:rank wikibase:NormalRank ;
	ps:P67 "CID11:5C52.11" .

wd:Q40066 p:P70 wds:Q40066-8426911F-535C-40A7-BCC7-76CDC0449FF3 .

wds:Q40066-8426911F-535C-40A7-BCC7-76CDC0449FF3 a wikibase:Statement,
		wikibase:BestRank ;
	wikibase:rank wikibase:NormalRank ;
	ps:P70 "dki-india-5C52.11" .

wd:Q40066 p:P86 wds:Q40066-84D59697-765F-4832-877C-CF7EADC89697 .

wds:Q40066-84D59697-765F-4832-877C-CF7EADC89697 a wikibase:Statement,
		wikibase:BestRank ;
	wikibase:rank wikibase:NormalRank ;
	ps:P86 "Concluído" .

wd:Q40066 p:P78 wds:Q40066-D24A5AA0-15CD-4FC1-A2AE-D69839CFADEB .

wds:Q40066-D24A5AA0-15CD-4FC1-A2AE-D69839CFADEB a wikibase:Statement,
		wikibase:BestRank ;
	wikibase:rank wikibase:NormalRank ;
	ps:P78 <https://pauloleads.com.br/cases-publicos/> .

wd:Q40066 p:P80 wds:Q40066-4A15E5BE-40E9-497C-9A64-DB24EF248F5F .

wds:Q40066-4A15E5BE-40E9-497C-9A64-DB24EF248F5F a wikibase:Statement,
		wikibase:BestRank ;
	wikibase:rank wikibase:NormalRank ;
	ps:P80 "2026-08-13T00:00:00Z"^^xsd:dateTime ;
	psv:P80 wdv:d79e909cd3fb623a2f2f7e2ef8a5c1a5 .

wd:Q40066 p:P89 wds:Q40066-A39A163E-7AFD-4B07-A3BB-0BA81C9A5999 .

wds:Q40066-A39A163E-7AFD-4B07-A3BB-0BA81C9A5999 a wikibase:Statement,
		wikibase:BestRank ;
	wikibase:rank wikibase:NormalRank ;
	ps:P89 wd:Q15613 .

wd:Q40066 rdfs:label "5C52.11"@mul ;
	skos:prefLabel "5C52.11"@mul ;
	schema:name "5C52.11"@mul ;
	rdfs:label "Defeito na síntese de ácido biliar com colestase"@pt-br ;
	skos:prefLabel "Defeito na síntese de ácido biliar com colestase"@pt-br ;
	schema:name "Defeito na síntese de ácido biliar com colestase"@pt-br ;
	rdfs:label "Bile acid synthesis defect with cholestasis"@en ;
	skos:prefLabel "Bile acid synthesis defect with cholestasis"@en ;
	schema:name "Bile acid synthesis defect with cholestasis"@en ;
	schema:description "As anomalias da síntese do ácido biliar são um grupo de distúrbios do metabolismo do esterol devido a deficiências enzimáticas da síntese do ácido biliar em bebês, crianças e adultos, com manifestações variáveis ​​que incluem colestase, doença neurológica e má absorção de gordura.Oito erros inatos foram identificados, 7 dos quais levam à colestase hepática e incluem: deficiência de oxidoredutase de 3-beta-hidroxi-C27-esteróide (tipo 1), deficiência de delta4-3-oxosteriode-5-beta redutase (tipo 2), deficiência de oxisterol 7alfa-hidroxilase (tipo 3), deficiência de 2-metilacil-CoA racemase (tipo 4), deficiência de ácido biliar CoA ligase e xantomatose cerebrotendínea. A deficiência de colesterol 7alfa-hidroxilase leva à hipercolesterolemia sem colestase hepática."@pt-br,
		"Anomalies of bile acid synthesis are a group of sterol metabolism disorders due to enzyme deficiencies of bile acid synthesis in infants, children and adults, with variable manifestations that include cholestasis, neurological disease, and fat malabsorption. Eight inborn errors have been clearly identified, 7 of which lead to liver cholestasis and include: 3β-hydroxy-C27-steroid oxidoreductase deficiency (type 1), Δ4-3-oxosteroid 5β-reductase deficiency (type 2), oxysterol 7α-hydroxylase deficiency (type 3), 2-methylacyl-CoA racemase deficiency (type 4), bile acid CoA ligase deficiency, and cerebrotendinous xanthomatosis. Cholesterol 7α-hydroxylase deficiency leads to hypercholesterolaemia without liver cholestasis."@en .

wd:P68 a wikibase:Property ;
	rdfs:label "Canonical URI"@en ;
	skos:prefLabel "Canonical URI"@en ;
	schema:name "Canonical URI"@en ;
	rdfs:label "URI"@mul ;
	skos:prefLabel "URI"@mul ;
	schema:name "URI"@mul ;
	schema:description "Canonical and absolute URI that resolves the entity in the semantic web."@en ;
	wikibase:propertyType <http://wikiba.se/ontology#Url> ;
	wikibase:directClaim wdt:P68 ;
	wikibase:claim p:P68 ;
	wikibase:statementProperty ps:P68 ;
	wikibase:statementValue psv:P68 ;
	wikibase:qualifier pq:P68 ;
	wikibase:qualifierValue pqv:P68 ;
	wikibase:reference pr:P68 ;
	wikibase:referenceValue prv:P68 ;
	wikibase:novalue wdno:P68 .

p:P68 a owl:ObjectProperty .

psv:P68 a owl:ObjectProperty .

pqv:P68 a owl:ObjectProperty .

prv:P68 a owl:ObjectProperty .

wdt:P68 a owl:ObjectProperty .

ps:P68 a owl:ObjectProperty .

pq:P68 a owl:ObjectProperty .

pr:P68 a owl:ObjectProperty .

wdno:P68 a owl:Class ;
	owl:complementOf _:876f845b5aa9df46c3769410b4980ef2 .

_:876f845b5aa9df46c3769410b4980ef2 a owl:Restriction ;
	owl:onProperty wdt:P68 ;
	owl:someValuesFrom owl:Thing .

wd:P67 a wikibase:Property ;
	rdfs:label "CURIE"@en ;
	skos:prefLabel "CURIE"@en ;
	schema:name "CURIE"@en ;
	rdfs:label "CURIE"@mul ;
	skos:prefLabel "CURIE"@mul ;
	schema:name "CURIE"@mul ;
	schema:description "Compact URI prefix identifier for serialization in ontologies and RDF."@en ;
	wikibase:propertyType <http://wikiba.se/ontology#String> ;
	wikibase:directClaim wdt:P67 ;
	wikibase:claim p:P67 ;
	wikibase:statementProperty ps:P67 ;
	wikibase:statementValue psv:P67 ;
	wikibase:qualifier pq:P67 ;
	wikibase:qualifierValue pqv:P67 ;
	wikibase:reference pr:P67 ;
	wikibase:referenceValue prv:P67 ;
	wikibase:novalue wdno:P67 .

p:P67 a owl:ObjectProperty .

psv:P67 a owl:ObjectProperty .

pqv:P67 a owl:ObjectProperty .

prv:P67 a owl:ObjectProperty .

wdt:P67 a owl:DatatypeProperty .

ps:P67 a owl:DatatypeProperty .

pq:P67 a owl:DatatypeProperty .

pr:P67 a owl:DatatypeProperty .

wdno:P67 a owl:Class ;
	owl:complementOf _:fb4af2e463edc3c5bcfdd04432e3ed85 .

_:fb4af2e463edc3c5bcfdd04432e3ed85 a owl:Restriction ;
	owl:onProperty wdt:P67 ;
	owl:someValuesFrom owl:Thing .

wd:P70 a wikibase:Property ;
	rdfs:label "Canary Token"@en ;
	skos:prefLabel "Canary Token"@en ;
	schema:name "Canary Token"@en ;
	rdfs:label "Canary Token"@mul ;
	skos:prefLabel "Canary Token"@mul ;
	schema:name "Canary Token"@mul ;
	schema:description "Tracking token intentionally inserted to audit data leaks, scraping, or unauthorized AI usage."@en ;
	wikibase:propertyType <http://wikiba.se/ontology#String> ;
	wikibase:directClaim wdt:P70 ;
	wikibase:claim p:P70 ;
	wikibase:statementProperty ps:P70 ;
	wikibase:statementValue psv:P70 ;
	wikibase:qualifier pq:P70 ;
	wikibase:qualifierValue pqv:P70 ;
	wikibase:reference pr:P70 ;
	wikibase:referenceValue prv:P70 ;
	wikibase:novalue wdno:P70 .

p:P70 a owl:ObjectProperty .

psv:P70 a owl:ObjectProperty .

pqv:P70 a owl:ObjectProperty .

prv:P70 a owl:ObjectProperty .

wdt:P70 a owl:DatatypeProperty .

ps:P70 a owl:DatatypeProperty .

pq:P70 a owl:DatatypeProperty .

pr:P70 a owl:DatatypeProperty .

wdno:P70 a owl:Class ;
	owl:complementOf _:311fb3b1dabc1cc8a6bb7feafe7ab91b .

_:311fb3b1dabc1cc8a6bb7feafe7ab91b a owl:Restriction ;
	owl:onProperty wdt:P70 ;
	owl:someValuesFrom owl:Thing .

wd:P86 a wikibase:Property ;
	rdfs:label "Verification Status"@en ;
	skos:prefLabel "Verification Status"@en ;
	schema:name "Verification Status"@en ;
	rdfs:label "Status de Verificação"@mul ;
	skos:prefLabel "Status de Verificação"@mul ;
	schema:name "Status de Verificação"@mul ;
	schema:description "Current data verification status of the entity."@en ;
	wikibase:propertyType <http://wikiba.se/ontology#String> ;
	wikibase:directClaim wdt:P86 ;
	wikibase:claim p:P86 ;
	wikibase:statementProperty ps:P86 ;
	wikibase:statementValue psv:P86 ;
	wikibase:qualifier pq:P86 ;
	wikibase:qualifierValue pqv:P86 ;
	wikibase:reference pr:P86 ;
	wikibase:referenceValue prv:P86 ;
	wikibase:novalue wdno:P86 .

p:P86 a owl:ObjectProperty .

psv:P86 a owl:ObjectProperty .

pqv:P86 a owl:ObjectProperty .

prv:P86 a owl:ObjectProperty .

wdt:P86 a owl:DatatypeProperty .

ps:P86 a owl:DatatypeProperty .

pq:P86 a owl:DatatypeProperty .

pr:P86 a owl:DatatypeProperty .

wdno:P86 a owl:Class ;
	owl:complementOf _:09f280a5f3614935b96ccb8c5d63b022 .

_:09f280a5f3614935b96ccb8c5d63b022 a owl:Restriction ;
	owl:onProperty wdt:P86 ;
	owl:someValuesFrom owl:Thing .

wd:P78 a wikibase:Property ;
	rdfs:label "Knowledge Architect"@en ;
	skos:prefLabel "Knowledge Architect"@en ;
	schema:name "Knowledge Architect"@en ;
	rdfs:label "Engº de dados"@mul ;
	skos:prefLabel "Engº de dados"@mul ;
	schema:name "Engº de dados"@mul ;
	schema:description "Knowledge engineer responsible for the curation, ontological modeling, and DKI structuring of this record."@en ;
	wikibase:propertyType <http://wikiba.se/ontology#Url> ;
	wikibase:directClaim wdt:P78 ;
	wikibase:claim p:P78 ;
	wikibase:statementProperty ps:P78 ;
	wikibase:statementValue psv:P78 ;
	wikibase:qualifier pq:P78 ;
	wikibase:qualifierValue pqv:P78 ;
	wikibase:reference pr:P78 ;
	wikibase:referenceValue prv:P78 ;
	wikibase:novalue wdno:P78 .

p:P78 a owl:ObjectProperty .

psv:P78 a owl:ObjectProperty .

pqv:P78 a owl:ObjectProperty .

prv:P78 a owl:ObjectProperty .

wdt:P78 a owl:ObjectProperty .

ps:P78 a owl:ObjectProperty .

pq:P78 a owl:ObjectProperty .

pr:P78 a owl:ObjectProperty .

wdno:P78 a owl:Class ;
	owl:complementOf _:2710e6edcea8e899ac7ae90ea2f8757a .

_:2710e6edcea8e899ac7ae90ea2f8757a a owl:Restriction ;
	owl:onProperty wdt:P78 ;
	owl:someValuesFrom owl:Thing .

wd:P80 a wikibase:Property ;
	rdfs:label "Collection date"@en ;
	skos:prefLabel "Collection date"@en ;
	schema:name "Collection date"@en ;
	rdfs:label "data da última verificação"@mul ;
	skos:prefLabel "data da última verificação"@mul ;
	schema:name "data da última verificação"@mul ;
	schema:description "Date the data was last collected or verified."@en ;
	wikibase:propertyType <http://wikiba.se/ontology#Time> ;
	wikibase:directClaim wdt:P80 ;
	wikibase:claim p:P80 ;
	wikibase:statementProperty ps:P80 ;
	wikibase:statementValue psv:P80 ;
	wikibase:qualifier pq:P80 ;
	wikibase:qualifierValue pqv:P80 ;
	wikibase:reference pr:P80 ;
	wikibase:referenceValue prv:P80 ;
	wikibase:novalue wdno:P80 .

p:P80 a owl:ObjectProperty .

psv:P80 a owl:ObjectProperty .

pqv:P80 a owl:ObjectProperty .

prv:P80 a owl:ObjectProperty .

wdt:P80 a owl:DatatypeProperty .

ps:P80 a owl:DatatypeProperty .

pq:P80 a owl:DatatypeProperty .

pr:P80 a owl:DatatypeProperty .

wdno:P80 a owl:Class ;
	owl:complementOf _:66cf0dd736f1df9217b0a14beb1128c8 .

_:66cf0dd736f1df9217b0a14beb1128c8 a owl:Restriction ;
	owl:onProperty wdt:P80 ;
	owl:someValuesFrom owl:Thing .

wd:Q15613 a wikibase:Item ;
	rdfs:label "E75"@mul ;
	skos:prefLabel "E75"@mul ;
	schema:name "E75"@mul ;
	schema:description "Disorders of sphingolipid metabolism and other lipid storage disorders"@en .

wd:P89 a wikibase:Property ;
	rdfs:label "Linked ICD 10"@en ;
	skos:prefLabel "Linked ICD 10"@en ;
	schema:name "Linked ICD 10"@en ;
	rdfs:label "CID 10 Vinculado"@mul ;
	skos:prefLabel "CID 10 Vinculado"@mul ;
	schema:name "CID 10 Vinculado"@mul ;
	schema:description "International Classification of Diseases node linked to the entity."@en ;
	wikibase:propertyType <http://wikiba.se/ontology#WikibaseItem> ;
	wikibase:directClaim wdt:P89 ;
	wikibase:claim p:P89 ;
	wikibase:statementProperty ps:P89 ;
	wikibase:statementValue psv:P89 ;
	wikibase:qualifier pq:P89 ;
	wikibase:qualifierValue pqv:P89 ;
	wikibase:reference pr:P89 ;
	wikibase:referenceValue prv:P89 ;
	wikibase:novalue wdno:P89 .

p:P89 a owl:ObjectProperty .

psv:P89 a owl:ObjectProperty .

pqv:P89 a owl:ObjectProperty .

prv:P89 a owl:ObjectProperty .

wdt:P89 a owl:ObjectProperty .

ps:P89 a owl:ObjectProperty .

pq:P89 a owl:ObjectProperty .

pr:P89 a owl:ObjectProperty .

wdno:P89 a owl:Class ;
	owl:complementOf _:2b1b3c83209df749f1e16974220adf10 .

_:2b1b3c83209df749f1e16974220adf10 a owl:Restriction ;
	owl:onProperty wdt:P89 ;
	owl:someValuesFrom owl:Thing .

wdv:d79e909cd3fb623a2f2f7e2ef8a5c1a5 a wikibase:TimeValue ;
	wikibase:timeValue "2026-08-13T00:00:00Z"^^xsd:dateTime ;
	wikibase:timePrecision "11"^^xsd:integer ;
	wikibase:timeTimezone "0"^^xsd:integer ;
	wikibase:timeCalendarModel <http://www.wikidata.org/entity/Q1985727> .