{"entities":{"Q40055":{"pageid":30423,"ns":120,"title":"Item:Q40055","lastrevid":126198,"modified":"2026-08-13T05:42:52Z","type":"item","id":"Q40055","labels":{"mul":{"language":"mul","value":"5C61.3"},"pt-br":{"language":"pt-br","value":"Defici\u00eancia de trealase"},"en":{"language":"en","value":"Alpha, alpha trehalase deficiency"}},"descriptions":{"pt-br":{"language":"pt-br","value":"A defici\u00eancia de trealase \u00e9 caracterizada por diarreia e v\u00f4mitos ap\u00f3s a ingest\u00e3o de trealose, um dissacar\u00eddeo encontrado principalmente em cogumelos. A doen\u00e7a \u00e9 muito rara na maioria das popula\u00e7\u00f5es, mas a incid\u00eancia foi estimada em pelo menos 1 em 13 na Groenl\u00e2ndia. A intoler\u00e2ncia \u00e0 trealose isolada \u00e9 devida a uma defici\u00eancia de trealase (TREH; 11q23.3), uma glicoprote\u00edna de membrana do tipo borda em escova."},"en":{"language":"en","value":"Alpha, alpha trehalase deficiency is characterised by diarrhoea and vomiting after ingestion of trehalose, a disaccharide found mainly in mushrooms. The disease is very rare in most populations but the incidence has been estimated at least 1 in 13 in Greenland. Isolated trehalose intolerance is due to a deficiency of trehalase (TREH; 11q23.3), a brush-border membrane glycoprotein."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"989b6c4156a387ed6caacf3b4c1c38bb0494a802","datavalue":{"value":"https://id.who.int/icd/entity/2025219157","type":"string"},"datatype":"url"},"type":"statement","id":"Q40055$999E4BDC-A236-463E-BF6E-1F6F235FBB79","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"bcf8d2e86a2849146868e9a0671f6bbace97fbe8","datavalue":{"value":"CID11:5C61.3","type":"string"},"datatype":"string"},"type":"statement","id":"Q40055$F0C1E3C6-3F40-4C8B-BB17-4FF45834891F","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"60e4de297a1372c51ecff435d4ebd6303538b25a","datavalue":{"value":"dki-india-5C61.3","type":"string"},"datatype":"string"},"type":"statement","id":"Q40055$E3CF8634-BA70-46F4-8AF7-5A12A060D068","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q40055$25674F5F-6D3C-4272-95BA-348082170130","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q40055$93374C63-8B57-4E7F-86F6-2E5AC9203287","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q40055$7D5F5EB7-DDA7-4C31-BE26-5EC0B59A1464","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"f25bc914ea31f0175652376fc1e7e98bd0c9c0c3","datavalue":{"value":{"entity-type":"item","numeric-id":15609,"id":"Q15609"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q40055$8E1D66E4-3FE3-4386-9F54-0FFE23668D57","rank":"normal"}]},"sitelinks":{}}}}