{"entities":{"Q39840":{"pageid":30208,"ns":120,"title":"Item:Q39840","lastrevid":124207,"modified":"2026-08-13T05:23:59Z","type":"item","id":"Q39840","labels":{"mul":{"language":"mul","value":"5A60.0"},"pt-br":{"language":"pt-br","value":"Acromegalia ou gigantismo hipofis\u00e1rio"},"en":{"language":"en","value":"Acromegaly or pituitary gigantism"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Acromegalia \u00e9 um dist\u00farbio adquirido relacionado \u00e0 produ\u00e7\u00e3o excessiva de horm\u00f4nio do crescimento (GH) e caracterizado por desfigura\u00e7\u00e3o som\u00e1tica progressiva (envolvendo principalmente a face e extremidades) e manifesta\u00e7\u00f5es sist\u00eamicas. As principais caracter\u00edsticas cl\u00ednicas s\u00e3o extremidades alargadas (m\u00e3os e p\u00e9s), dedos grossos, alargados e atarracados e tecido mole espessado. A doen\u00e7a tamb\u00e9m tem consequ\u00eancias reumatol\u00f3gicas, cardiovasculares, respirat\u00f3rias e metab\u00f3licas que determinam o seu progn\u00f3stico. Na maioria dos casos, a acromegalia est\u00e1 relacionada a um adenoma hipofis\u00e1rio, puramente secretor de GH (60%) ou misto. A cirurgia transesfenoidal costuma ser o tratamento de primeira linha. Quando a cirurgia n\u00e3o corrige a hipersecre\u00e7\u00e3o de GH/IGF-I, o tratamento com an\u00e1logos da somatostatina e/ou radioterapia pode ser usado."},"en":{"language":"en","value":"Acromegaly is an acquired disorder related to excessive production of growth hormone (GH) and characterised by progressive somatic disfigurement (mainly involving the face and extremities) and systemic manifestations. The main clinical features are broadened extremities (hands and feet), widened thickened and stubby fingers, and thickened soft tissue. The disease also has rheumatologic, cardiovascular, respiratory and metabolic consequences which determine its prognosis. In the majority of cases, acromegaly is related to a pituitary adenoma, either purely GH-secreting (60%) or mixed. Transsphenoidal surgery is often the first-line treatment. When surgery fails to correct GH/IGF-I hypersecretion, medical treatment with somatostatin analogs and/or radiotherapy can be used."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"4bd566f082b6ce9c3e3d5d7337c3ca26f221709c","datavalue":{"value":"https://id.who.int/icd/entity/825410563","type":"string"},"datatype":"url"},"type":"statement","id":"Q39840$13F0786B-A09B-4C2D-968A-B54C3F46DC7D","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"845dabbf59ccbdf62f1f0465f8f31ff970392dd8","datavalue":{"value":"CID11:5A60.0","type":"string"},"datatype":"string"},"type":"statement","id":"Q39840$3DF7579E-7134-4AFE-B107-50314EA8C84E","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"05bc4d0d264e9e4e6a46ea4bbcf11848a9e6ba3b","datavalue":{"value":"dki-india-5A60.0","type":"string"},"datatype":"string"},"type":"statement","id":"Q39840$B813A5CD-7B34-428E-AFF5-6896A37F4D7D","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q39840$2C63A36A-D468-42D1-BBF5-E749733ED414","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q39840$7B763FE6-1547-4483-87DF-CB5671279151","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q39840$51CFBD23-033E-4E73-8B46-A691E7A58495","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"830f7969547bedc817302033d3eddd59b3a291c7","datavalue":{"value":{"entity-type":"item","numeric-id":15227,"id":"Q15227"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q39840$92669A8A-6700-4A0A-A0DD-670D604F5B0D","rank":"normal"}]},"sitelinks":{}}}}