{"entities":{"Q39703":{"pageid":30071,"ns":120,"title":"Item:Q39703","lastrevid":123055,"modified":"2026-08-13T05:13:24Z","type":"item","id":"Q39703","labels":{"mul":{"language":"mul","value":"4A00.14"},"pt-br":{"language":"pt-br","value":"Angioedema heredit\u00e1rio"},"en":{"language":"en","value":"Hereditary angioedema"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Angioedema heredit\u00e1rio \u00e9 causado na maioria dos casos por baixos n\u00edveis absolutos (tipo I) ou funcionais (tipo II) geneticamente determinados do inibidor de C1, um inibidor da proteinase plasm\u00e1tica envolvido na regula\u00e7\u00e3o da ativa\u00e7\u00e3o do complemento. \u00c9 caracterizado clinicamente por edema subcut\u00e2neo e/ou submucoso recorrente e pode resultar em obstru\u00e7\u00e3o lar\u00edngea com risco de vida. O envolvimento do trato digestivo geralmente causa dor abdominal. Isso e a aus\u00eancia de p\u00e1pulas urticariformes ou coceira a distinguem da forma comum de angioedema, que faz parte do espectro da urtic\u00e1ria."},"en":{"language":"en","value":"Hereditary angioedema is caused in the majority of cases by genetically determined low absolute (type I) or functional (type II) levels of C1 inhibitor, a plasma proteinase inhibitor involved in regulation of complement activation. It is characterised clinically by recurrent subcutaneous and/or submucosal oedema and can result in life-threatening laryngeal obstruction. Involvement of the digestive tract commonly causes abdominal pain. This and the absence of accompanying urticarial weals or itch distinguish it from the common form of angioedema, which is part of the spectrum of urticaria."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"285cce97581f7947aacc306a5ea2645ef103cb9f","datavalue":{"value":"https://id.who.int/icd/entity/795969334","type":"string"},"datatype":"url"},"type":"statement","id":"Q39703$72625582-1429-4B71-A954-C70563696DB7","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"bb4d0ec02adc3e216fb8259456f4bb9c7d08d137","datavalue":{"value":"CID11:4A00.14","type":"string"},"datatype":"string"},"type":"statement","id":"Q39703$337FBB27-0350-451B-AA4E-B3FC32CB3582","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"53e272a037a7c00d013772352dccb5f304ee8412","datavalue":{"value":"dki-india-4A00.14","type":"string"},"datatype":"string"},"type":"statement","id":"Q39703$2FFA7EEE-BB4F-4A6F-B33C-018E51A7CA1F","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q39703$654DC69E-1003-48CC-8BFE-A9C1B751FE89","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q39703$88001FAE-8D56-4A2F-9153-0F6ADE808319","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q39703$6A8212E6-8EE8-425E-B319-A0217CEEA07A","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"c8becdd33e46a4d0e552052e6953bb2aeec8b894","datavalue":{"value":{"entity-type":"item","numeric-id":14947,"id":"Q14947"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q39703$13828461-8B13-4D8B-8EB4-A5E30A21B224","rank":"normal"}]},"sitelinks":{}}}}