{"entities":{"Q39132":{"pageid":29498,"ns":120,"title":"Item:Q39132","lastrevid":118282,"modified":"2026-08-13T04:27:17Z","type":"item","id":"Q39132","labels":{"mul":{"language":"mul","value":"2A90.6"},"pt-br":{"language":"pt-br","value":"Linfoma extranodal de c\u00e9lulas NK/T, tipo nasal"},"en":{"language":"en","value":"Extranodal NK/T-cell lymphoma, nasal type"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Linfoma n\u00e3o Hodgkin de c\u00e9lulas T maduras, agressivo, predominantemente extranodal. \u00c9 caracterizada por um infiltrado celular frequentemente angioc\u00eantrico e angiodestrutivo composto por c\u00e9lulas NK/T positivas para o v\u00edrus Epstein-Barr (EBV). A cavidade nasal \u00e9 a localiza\u00e7\u00e3o de envolvimento mais comum. Os pacientes frequentemente apresentam les\u00f5es destrutivas na face m\u00e9dia (granuloma letal da linha m\u00e9dia). A doen\u00e7a pode se disseminar rapidamente para v\u00e1rias localiza\u00e7\u00f5es anat\u00f4micas, incluindo trato gastrointestinal, pele, test\u00edculos e linfonodos cervicais. \u00c9 tamb\u00e9m conhecido como linfoma de c\u00e9lulas T angioc\u00eantrico. O termo reticulose polim\u00f3rfica tem sido amplamente utilizado para descrever as altera\u00e7\u00f5es morfol\u00f3gicas observadas nesse tipo de linfoma. No entanto, este termo tamb\u00e9m pode ser aplicado \u00e0 granulomatose linfomatoide, que \u00e9 um transtorno linfoproliferativo de c\u00e9lulas B positivo para EBV angioc\u00eantrico e angiodestrutivo."},"en":{"language":"en","value":"An aggressive, predominantly extranodal, mature T-cell non-Hodgkin lymphoma. It is characterised by an often angiocentric and angiodestructive cellular infiltrate composed of Epstein-Barr Virus (EBV) positive NK/T cells. The nasal cavity is the most common site of involvement. Patients often present with midfacial destructive lesions (lethal midline granuloma). The disease may disseminate rapidly to various anatomic sites including the gastrointestinal tract, skin, testis, and cervical lymph nodes. It is also known as angiocentric T-cell lymphoma. The term polymorphic reticulosis has been widely used to describe the morphologic changes seen in this type of lymphoma. However, the latter term may also apply to lymphomatoid granulomatosis, which is an angiocentric and angiodestructive EBV positive B-cell lymphoproliferative disorder."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"df17bac5868ab24d2d5f2163c472bf5ab0c11131","datavalue":{"value":"https://id.who.int/icd/entity/684005900","type":"string"},"datatype":"url"},"type":"statement","id":"Q39132$FDFE85D0-7A13-4F69-A714-93FB84FF47A8","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"5f75e0dd22324f6941b45708158099f21f2dc0f0","datavalue":{"value":"CID11:2A90.6","type":"string"},"datatype":"string"},"type":"statement","id":"Q39132$51119B45-E358-453E-89B0-B0304A1ED5E6","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"ec4b2332b78f4dd49c13e3a537728e8645b07634","datavalue":{"value":"dki-india-2A90.6","type":"string"},"datatype":"string"},"type":"statement","id":"Q39132$A895F83F-AA6A-44CA-8B5A-5D82C284A33D","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q39132$6AB06525-4576-46D6-B9A4-D7B84EB4DACA","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q39132$1545C8A4-EB97-4B58-8A7B-0ECB6C97C4FA","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q39132$A2D0CA30-4E39-470D-82A6-3B3A42780FCC","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"c07018fda8ede4b732da3f72b34a3caba6002b48","datavalue":{"value":{"entity-type":"item","numeric-id":39131,"id":"Q39131"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q39132$3A84D5BC-3759-463A-A0CC-1B91EFAB1C2F","rank":"normal"}]},"sitelinks":{}}}}