{"entities":{"Q39015":{"pageid":29381,"ns":120,"title":"Item:Q39015","lastrevid":117429,"modified":"2026-08-13T04:19:08Z","type":"item","id":"Q39015","labels":{"mul":{"language":"mul","value":"2D11"},"pt-br":{"language":"pt-br","value":"Neoplasias malignas da gl\u00e2ndula adrenal"},"en":{"language":"en","value":"Malignant neoplasms of adrenal gland"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Os tumores que se originam do c\u00f3rtex adrenal incluem adenomas e carcinomas. Estas s\u00e3o neoplasias raras, mas podem causar uma s\u00e9rie de sintomas hormonais, incluindo hiperaldosteronismo, s\u00edndrome de Cushing e viriliza\u00e7\u00e3o. Uma pequena fra\u00e7\u00e3o dos tumores adrenocorticais est\u00e1 associada a uma s\u00edndrome tumoral heredit\u00e1ria, incluindo a s\u00edndrome de Li-Fraumeni e o complexo de Carney._x000D_ Feocromocitomas benignos e malignos surgem na medula adrenal e s\u00e3o derivados de c\u00e9lulas cromafins com origem na crista neural. Os feocromocitomas podem ocorrer no contexto de v\u00e1rias condi\u00e7\u00f5es heredit\u00e1rias, incluindo neoplasia end\u00f3crina m\u00faltipla dos tipos 2a e 2b, doen\u00e7a de von Hippel Lindau e neurofibromatose._x000D_ Os paragangliomas extra-adrenais se originam de c\u00e9lulas cromafins nos parag\u00e2nglios simpatoadrenais e parassimp\u00e1ticos. Eles ocorrem em muitas partes do corpo e podem representar um desafio significativo para cirurgi\u00f5es e oncologistas. Alguns funcionam como quimiorreceptores, outros s\u00e3o endocrinologicamente ativos. Os paragangliomas familiares est\u00e3o associados a muta\u00e7\u00f5es dos genes do complexo II mitocondrial."},"en":{"language":"en","value":"Tumours arising from the adrenal cortex include adenomas and carcinomas. These are rare neoplasms but may cause a variety of hormonal symptoms, including hyperaldosteronism, Cushing syndrome, and virilisation. A small fraction of adrenocortical tumours are associated with an inherited tumour syndrome, including Li-Fraumeni syndrome and Carney complex. Benign and malignant phaeochromocytomas arise in the adrenal medulla and are derived from chromaffin cells of neural crest origin. Phaeochromocytomas may occur in the setting of several hereditary conditions, including multiple endocrine neoplasia types 2a and 2b, von Hippel Lindau disease and neurofibromatosis. Extra adrenal paragangliomas arise from chromaffin cells in sympathoadrenal and parasympathetic paraganglia. They occur in many parts of the body and can pose a significant challenge to surgeons and oncologists. Some function as chemoreceptors, others are endocrinologically active. Familial paragangliomas are associated with mutations of the mitochondrial complex II genes."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"936754e6edf4c7a6207e955e68508be7561af8c8","datavalue":{"value":"https://id.who.int/icd/entity/1766185236","type":"string"},"datatype":"url"},"type":"statement","id":"Q39015$F98191CF-840F-4544-890E-CF520D9275BE","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"d7a1faca68175565eec29f621bb4ea145fa79129","datavalue":{"value":"CID11:2D11","type":"string"},"datatype":"string"},"type":"statement","id":"Q39015$B6C09BAB-A0FE-44D3-AF4D-E06D7FCF249B","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"19e0568fbb0d0e2b3a50cc125117334c538faf3a","datavalue":{"value":"dki-india-2D11","type":"string"},"datatype":"string"},"type":"statement","id":"Q39015$E0ACC468-495D-4C01-A31F-8A34C8AB73E6","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q39015$B91D57BC-21F8-437C-BD24-4E9C7F24FB47","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q39015$80D9BE7E-EAF9-42CC-90B2-657D9E43758C","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q39015$84F5ABD3-C508-43AA-B0A4-4A6108111250","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"f82632647ead92ab6f2bafa87daa01f2a1479a10","datavalue":{"value":{"entity-type":"item","numeric-id":13642,"id":"Q13642"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q39015$59619AD9-EFDD-47BC-9672-BA7990CBDE61","rank":"normal"}]},"sitelinks":{}}}}