{"entities":{"Q107590":{"pageid":97982,"ns":120,"title":"Item:Q107590","lastrevid":624593,"modified":"2026-08-17T14:35:32Z","type":"item","id":"Q107590","labels":{"mul":{"language":"mul","value":"ID_1696588973"},"pt-br":{"language":"pt-br","value":"Defeito do gene da subunidade estrutural do complexo III da cadeia respirat\u00f3ria mitocondrial"},"en":{"language":"en","value":"Mitochondrial respiratory chain complex III structural subunit gene defect"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Complexo III \u00e9 quando o ciclo Q contribui para o gradiente de pr\u00f3tons por uma absor\u00e7\u00e3o/libera\u00e7\u00e3o assim\u00e9trica de pr\u00f3tons. Dois el\u00e9trons s\u00e3o removidos de QH2 no local QO e sequencialmente transferidos para duas mol\u00e9culas de citocromo C, um transportador de el\u00e9trons sol\u00favel em \u00e1gua localizado dentro do espa\u00e7o intermembranar. Este diagn\u00f3stico \u00e9 com defeito do gene da subunidade estrutural."},"en":{"language":"en","value":"Complex III is when the Q-cycle contributes to the proton gradient by an asymmetric absorption/release of protons. Two electrons are removed from QH2 at the QO site and sequentially transferred to two molecules of cytochrome c, a water-soluble electron carrier located within the intermembrane space. This diagnosis is with structural subunit gene defect."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"808a854ba7530f4c5548b8ec36cb2881c2c681d5","datavalue":{"value":"https://id.who.int/icd/entity/1696588973","type":"string"},"datatype":"url"},"type":"statement","id":"Q107590$774F8E4C-F7A4-413C-B5FC-64A9928970AA","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"72a9afdef178b9e39b76d06fb736abf81fc49b74","datavalue":{"value":"CID11:ID_1696588973","type":"string"},"datatype":"string"},"type":"statement","id":"Q107590$3205ECAB-E2AB-46D8-ACB0-4D825169902B","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"64a534124504ca169ea42d730980e7d5a8b899f9","datavalue":{"value":"dki-india-ID_1696588973","type":"string"},"datatype":"string"},"type":"statement","id":"Q107590$5E6496D0-0C1A-43E2-BAEB-2923CC251C02","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q107590$434619FA-600E-4BBE-9864-1C4B117CBBE0","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q107590$1554F3B2-61BF-46B5-886D-8B72281ADCBC","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"8612011b2ca718e4ec0db5a49d2de6d25b2e811c","datavalue":{"value":{"time":"+2026-08-16T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q107590$5B8A9C4F-452A-41DD-88D6-C9F3891028C7","rank":"normal"}]},"sitelinks":{}}}}