{"entities":{"Q107372":{"pageid":97770,"ns":120,"title":"Item:Q107372","lastrevid":623056,"modified":"2026-08-17T14:22:04Z","type":"item","id":"Q107372","labels":{"mul":{"language":"mul","value":"ID_1041399919"},"pt-br":{"language":"pt-br","value":"Doen\u00e7a glomerular com doen\u00e7a de dep\u00f3sito denso"},"en":{"language":"en","value":"Glomerular disease with dense deposit disease"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Apresenta\u00e7\u00e3o glomerular espec\u00edfica com bandas densas de el\u00e9trons descont\u00ednuas dentro da membrana basal glomerular. Existe intensa colora\u00e7\u00e3o linear ou tipo banda na imunocolora\u00e7\u00e3o para o componente 3 do complemento (C3) com pouca ou nenhuma imunoglobulina. Anteriormente conhecida como glomerulonefrite membranoproliferativa Tipo II, mas na verdade a apar\u00eancia \u00e0 microscopia \u00f3ptica pode variar amplamente. A doen\u00e7a de dep\u00f3sito denso \u00e9 o resultado da ativa\u00e7\u00e3o da via alternativa do complemento associada, a ativa\u00e7\u00e3o descontrolada da C3 convertase. Em alguns casos, a lipodistrofia parcial tamb\u00e9m est\u00e1 associada."},"en":{"language":"en","value":"A specific glomerular appearance with discontinuous electron dense bands within the glomerular basement membrane. There is intense linear or band like immuno-staining for complement component 3 (C3) with little or no immunoglobulin. Previously known as Type II membranoproliferative glomerulonephritis but actually the light microscopic appearance can vary widely. Dense deposit disease is the result of activation of the alternative complement pathway associated, uncontrolled activation of C3 convertase. In some cases partial lipodystrophy is also associated."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"5f357de6a00d9fd33ad3948bf6814cf48b6bf7df","datavalue":{"value":"https://id.who.int/icd/entity/1041399919","type":"string"},"datatype":"url"},"type":"statement","id":"Q107372$5F5A5E12-3408-4ADF-BB2A-CD3D1632D517","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"690b0d62edc8b0b62d745593430ecc740fd4ba6a","datavalue":{"value":"CID11:ID_1041399919","type":"string"},"datatype":"string"},"type":"statement","id":"Q107372$84BBFEB5-FF67-46EE-B9E6-7FFFB4208DDC","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"d4f6d24978991f7d9a9547312cc5573406a08da0","datavalue":{"value":"dki-india-ID_1041399919","type":"string"},"datatype":"string"},"type":"statement","id":"Q107372$F16AA6BF-2D02-4CED-B46D-59A12D7D6B1A","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q107372$4F9F2E9B-538B-4554-BB10-FFF8122CDB54","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q107372$58EC2C42-F67D-455C-9090-4FCEAC8C6825","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"8612011b2ca718e4ec0db5a49d2de6d25b2e811c","datavalue":{"value":{"time":"+2026-08-16T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q107372$B8CBAFA6-137C-47EE-A00E-37579841AC89","rank":"normal"}]},"sitelinks":{}}}}