{"entities":{"Q107203":{"pageid":97601,"ns":120,"title":"Item:Q107203","lastrevid":621830,"modified":"2026-08-17T14:11:56Z","type":"item","id":"Q107203","labels":{"mul":{"language":"mul","value":"ID_2137578537"},"pt-br":{"language":"pt-br","value":"Doen\u00e7a de inclus\u00e3o das microvilosidades"},"en":{"language":"en","value":"Microvillous inclusion disease"}},"descriptions":{"pt-br":{"language":"pt-br","value":"A doen\u00e7a de inclus\u00e3o das microvilosidades (DIM) ou atrofia das microvilosidades \u00e9 um transtorno cong\u00eanito das c\u00e9lulas epiteliais intestinais que se apresenta com diarreia aquosa persistente com risco de vida e \u00e9 caracterizada por anormalidades morfol\u00f3gicas dos enter\u00f3citos. Este \u00e9 um transtorno gen\u00e9tico raro que \u00e9 herdado em um padr\u00e3o autoss\u00f4mico recessivo. \u00c9 causada por uma falta cong\u00eanita de microvilosidades apicais nas c\u00e9lulas epiteliais do intestino delgado, no entanto, geralmente n\u00e3o possui a infiltra\u00e7\u00e3o linfoc\u00edtica intraepitelial caracter\u00edstica do espru cel\u00edaco e apresenta colora\u00e7\u00e3o positiva para ant\u00edgeno carcinoembrion\u00e1rio (CEA)._x000D_ A DIM manifesta-se nos primeiros dias de vida (forma de in\u00edcio precoce) ou nos primeiros dois meses (forma de in\u00edcio tardio) de vida."},"en":{"language":"en","value":"Microvillous inclusion disease (MVID) or microvillous atrophy is a congenital disorder of the intestinal epithelial cells that presents with persistent life-threatening watery diarrhoea and is characterised by morphological enterocyte abnormalities. This is a rare genetic disorder that is inherited in an autosomal recessive pattern. It is caused by a congenital lack of apical microvilli in the epithelial cells of the small intestine, however, it usually lacks the intraepithelial lymphocytic infiltration characteristic of celiac sprue and stains positive for carcinoembryonic antigen (CEA). MVID manifests either in the first days of life (early-onset form) or in the first two months (late-onset form) of life."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"be27e1e43e2501e88ee903ef62ab9289ccd9f41e","datavalue":{"value":"https://id.who.int/icd/entity/2137578537","type":"string"},"datatype":"url"},"type":"statement","id":"Q107203$47375C22-7742-4EB2-B187-10DBE2C2AA02","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"57a687f71401167b479145945f527f9564a34947","datavalue":{"value":"CID11:ID_2137578537","type":"string"},"datatype":"string"},"type":"statement","id":"Q107203$39B0EB38-EE4D-4AD4-94E9-5A1B60D76350","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"38c78fe166e1d5f9848f5cbcb883096926d1818b","datavalue":{"value":"dki-india-ID_2137578537","type":"string"},"datatype":"string"},"type":"statement","id":"Q107203$54D8DA34-2393-4AF4-ADEE-CBCE778AEB07","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q107203$3296CBA0-EBAC-428D-91B5-9972D1DC35B0","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q107203$88CCA9A2-B4AC-4C95-9475-D3E874992251","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"8612011b2ca718e4ec0db5a49d2de6d25b2e811c","datavalue":{"value":{"time":"+2026-08-16T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q107203$696E87AF-FAF2-4947-89CD-C557289EEE2A","rank":"normal"}]},"sitelinks":{}}}}