{"entities":{"Q105608":{"pageid":96006,"ns":120,"title":"Item:Q105608","lastrevid":610417,"modified":"2026-08-17T11:57:02Z","type":"item","id":"Q105608","labels":{"mul":{"language":"mul","value":"ID_2111612055"},"pt-br":{"language":"pt-br","value":"S\u00edndrome cora\u00e7\u00e3o-m\u00e3o tipo 2"},"en":{"language":"en","value":"Heart-hand syndrome type 2"}},"descriptions":{"pt-br":{"language":"pt-br","value":"S\u00edndrome cora\u00e7\u00e3o-m\u00e3o tipo 2 \u00e9 uma s\u00edndrome cora\u00e7\u00e3o-m\u00e3o extremamente rara descrita em duas fam\u00edlias at\u00e9 o momento, que \u00e9 caracterizada por malforma\u00e7\u00f5es dos membros superiores (braquitelefalangia tipo D, delt\u00f3ides hipopl\u00e1sicos, leve encurtamento do quarto e quinto metacarpos em alguns indiv\u00edduos, anomalias esquel\u00e9ticas em \u00famero, r\u00e1dio, ulna e ossos tenares) e arritmias card\u00edacas (ritmos juncionais e fibrila\u00e7\u00e3o atrial)."},"en":{"language":"en","value":"Heart-hand syndrome type 2 is an extremely rare heart-hand syndrome described in two families to date, that is characterised by upper limb malformations (brachytelephalangy type D, hypoplastic deltoids, mild shortening of the fourth and fifth metacarpals in some individuals, skeletal anomalies in the humerus, radius, ulnae, and thenar bones) and cardiac arrhythmias (junctional rhythms and atrial fibrillation)."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"05df26b2057aea600e18bbf26004ab3de7dbffef","datavalue":{"value":"https://id.who.int/icd/entity/2111612055","type":"string"},"datatype":"url"},"type":"statement","id":"Q105608$FC3EDA13-EE20-41CE-A03B-B8BF7CDFCDA1","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"8fc098cb0046013300b53a673fccbbd07388bcff","datavalue":{"value":"CID11:ID_2111612055","type":"string"},"datatype":"string"},"type":"statement","id":"Q105608$89F41FF2-618E-497A-9DE1-0B475BDF796D","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"07bbcbeaafe2b6e54283b529c814c943bf14003c","datavalue":{"value":"dki-india-ID_2111612055","type":"string"},"datatype":"string"},"type":"statement","id":"Q105608$A9F6A50A-8CD0-4AD5-A900-05391DF3C3A2","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q105608$E6FC2329-E47B-43FB-A682-CE7589FBD0E9","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q105608$A29CA7C7-1A7F-461A-8A92-0D7E29978969","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"8612011b2ca718e4ec0db5a49d2de6d25b2e811c","datavalue":{"value":{"time":"+2026-08-16T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q105608$806BA353-2379-4371-B401-795CD6E44830","rank":"normal"}]},"sitelinks":{}}}}