{"entities":{"Q104321":{"pageid":94719,"ns":120,"title":"Item:Q104321","lastrevid":601165,"modified":"2026-08-17T10:10:57Z","type":"item","id":"Q104321","labels":{"mul":{"language":"mul","value":"ID_792094526"},"pt-br":{"language":"pt-br","value":"Papulose atr\u00f3fica maligna"},"en":{"language":"en","value":"Malignant atrophic papulosis"}},"descriptions":{"pt-br":{"language":"pt-br","value":"A doen\u00e7a de Degos (papulose atr\u00f3fica maligna) \u00e9 uma vasculopatia oclusiva progressiva rara, de causa desconhecida, que afeta art\u00e9rias de pequeno e m\u00e9dio calibre. Suas manifesta\u00e7\u00f5es vari\u00e1veis resultam de infarto tecidual focal na pele e em outros \u00f3rg\u00e3os. Apresenta-se inicialmente na pele como pequenas p\u00e1pulas r\u00f3seas espalhadas que sofrem necrose isqu\u00eamica e deixam cicatrizes circulares caracter\u00edsticas, de cor branco-porcelana. Embora possa permanecer limitada \u00e0 pele, tende a progredir com o tempo para envolver outros sistemas org\u00e2nicos. M\u00faltiplos infartos focais no SNC podem resultar em uma ampla variedade de sequelas neurol\u00f3gicas. Hemorragia e perfura\u00e7\u00e3o gastrintestinal s\u00e3o as causas mais comuns de morte."},"en":{"language":"en","value":"Degos' disease (malignant atrophic papulosis) is a rare, progressive occlusive vasculopathy of unknown cause affecting small and medium calibre arteries. Its protean manifestations result from focal tissue infarction in skin and other organs. It presents initially in the skin as scattered small pink papules which undergo ischaemic necrosis to leave characteristic circular porcelain-white scars. Although it may remain limited to the skin, it tends over time to progress to involve other organ systems. Multiple focal infarcts in the CNS may result in a wide variety of neurological sequelae. Gastrointestinal bleeding and perforation are the most common causes of death."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"784140c0b64e6e309f70dc44294729ee34cc93e8","datavalue":{"value":"https://id.who.int/icd/entity/792094526","type":"string"},"datatype":"url"},"type":"statement","id":"Q104321$E2FC83EA-0A9D-4F7E-9270-2B30563CF8F5","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"8a82fed372aa931ce7b872f1b446caaddf299899","datavalue":{"value":"CID11:ID_792094526","type":"string"},"datatype":"string"},"type":"statement","id":"Q104321$54F568DD-1C5D-4118-946C-3A327A17F793","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"eac5fc1af9f478110ffa1a47d88238c361af3e02","datavalue":{"value":"dki-india-ID_792094526","type":"string"},"datatype":"string"},"type":"statement","id":"Q104321$94625A12-9C73-430F-B4E1-F3381D43E085","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q104321$A72F2321-4344-4C97-AC28-1B2FB2CE3EE5","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q104321$E10C0346-5026-4BB0-BB41-66D0A715F848","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"8612011b2ca718e4ec0db5a49d2de6d25b2e811c","datavalue":{"value":{"time":"+2026-08-16T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q104321$2D96A8CC-0CF8-4FA4-957B-F28E924488C0","rank":"normal"}]},"sitelinks":{}}}}