{"entities":{"Q102700":{"pageid":93093,"ns":120,"title":"Item:Q102700","lastrevid":589415,"modified":"2026-08-16T19:54:03Z","type":"item","id":"Q102700","labels":{"mul":{"language":"mul","value":"ID_1395443519"},"pt-br":{"language":"pt-br","value":"Agamaglobulinemia autoss\u00f4mica recessiva"},"en":{"language":"en","value":"Autosomal recessive agammaglobulinaemia"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Agamaglobulinemia autoss\u00f4mica \u00e9 uma defici\u00eancia imunol\u00f3gica prim\u00e1ria caracterizada por uma completa falta de c\u00e9lulas B maduras circulantes, resultando em agamaglobulinemia levando a uma suscetibilidade particular a infec\u00e7\u00f5es bacterianas dos tratos respirat\u00f3rio e digestivo. A meningoencefalite enteroviral \u00e9 uma complica\u00e7\u00e3o muito grave e comum."},"en":{"language":"en","value":"Autosomal agammaglobulinemia is a primary immune deficiency characterised by a complete lack of circulating mature B cells, resulting in agammaglobulinemia leading to particular susceptibility to bacterial infections of the respiratory and digestive tracts. Enteroviral meningo-encephalitis is a very severe and not infrequent complication."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"43c45109591d000338a6eed47e76de899d7c8846","datavalue":{"value":"https://id.who.int/icd/entity/1395443519","type":"string"},"datatype":"url"},"type":"statement","id":"Q102700$07D994F2-2CE8-49B1-A705-2FABF0F6B889","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"bca188390c53174f6c8660f0c5ce1683da2a7cfa","datavalue":{"value":"CID11:ID_1395443519","type":"string"},"datatype":"string"},"type":"statement","id":"Q102700$8E2D2295-E7F5-40E7-86F5-CF177BE1376B","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"7e19eb22deea0dd505ca36b9d195ff83e5c86fdc","datavalue":{"value":"dki-india-ID_1395443519","type":"string"},"datatype":"string"},"type":"statement","id":"Q102700$E9CD2C7A-E6BE-43E0-99A2-4317740136E0","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q102700$6EED9863-3616-4369-8B13-9BCECB5DF842","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q102700$4ACCB632-C941-4B0D-B90C-B566489FBA7D","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"378ac503ed43f21e1f461d2823a6ad59da580514","datavalue":{"value":{"time":"+2026-08-15T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q102700$3219FD98-FE49-442F-A453-9F85612D1C31","rank":"normal"}]},"sitelinks":{}}}}