{"entities":{"Q102302":{"pageid":92695,"ns":120,"title":"Item:Q102302","lastrevid":586579,"modified":"2026-08-16T19:14:27Z","type":"item","id":"Q102302","labels":{"mul":{"language":"mul","value":"ID_67580224"},"pt-br":{"language":"pt-br","value":"Defici\u00eancia isolada do complexo I da cadeia respirat\u00f3ria mitocondrial"},"en":{"language":"en","value":"Isolated mitochondrial respiratory chain complex I deficiency"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Trata-se da transfer\u00eancia de el\u00e9trons acoplada isolada entre um doador de el\u00e9trons (como NADH) e um aceptor de el\u00e9trons (como O2) com a transfer\u00eancia de \u00edons H + (pr\u00f3tons) atrav\u00e9s de uma membrana. Este diagn\u00f3stico \u00e9 com defici\u00eancia no Complexo I quando dois el\u00e9trons s\u00e3o removidos do NADH e transferidos para um carreador lipossol\u00favel, a ubiquinona (Q)."},"en":{"language":"en","value":"This refers to isolated coupled electron transfer between an electron donor (such as NADH) and an electron acceptor (such as O2) with the transfer of H+ ions (protons) across a membrane. This diagnosis is with deficiency in Complex I when two electrons are removed from NADH and transferred to a lipid-soluble carrier, ubiquinone (Q)."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"cc6beaccbb4c04c7d9ad8820e0ecc12c82935253","datavalue":{"value":"https://id.who.int/icd/entity/67580224","type":"string"},"datatype":"url"},"type":"statement","id":"Q102302$884F9DCA-0B90-4344-8CBD-D3C11AFE7511","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"6534f0330ddc056bed323706e1d95b9b123dba59","datavalue":{"value":"CID11:ID_67580224","type":"string"},"datatype":"string"},"type":"statement","id":"Q102302$29032834-2056-4DE6-872F-FFAE4DD2404C","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"7b625176560408ba5ef63fe8e244cda750649454","datavalue":{"value":"dki-india-ID_67580224","type":"string"},"datatype":"string"},"type":"statement","id":"Q102302$4A9B3936-D3BC-4A2A-BBDB-053B9B09B590","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q102302$E5E269A4-6CC9-4E56-B729-5B75708A4569","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q102302$B1621844-4C41-4B45-818D-47A363E33E6F","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"378ac503ed43f21e1f461d2823a6ad59da580514","datavalue":{"value":{"time":"+2026-08-15T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q102302$4D27B3B4-C90C-4450-B7C6-67D49DB3945E","rank":"normal"}]},"sitelinks":{}}}}