{"entities":{"Q102297":{"pageid":92690,"ns":120,"title":"Item:Q102297","lastrevid":586541,"modified":"2026-08-16T19:14:09Z","type":"item","id":"Q102297","labels":{"mul":{"language":"mul","value":"ID_369066691"},"pt-br":{"language":"pt-br","value":"Defici\u00eancia do complexo II da cadeia respirat\u00f3ria mitocondrial isolada"},"en":{"language":"en","value":"Isolated mitochondrial respiratory chain complex II deficiency"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Trata-se da transfer\u00eancia de el\u00e9trons acoplada isolada entre um doador de el\u00e9trons (como NADH) e receptor/ aceptor de el\u00e9trons (como O2) com a transfer\u00eancia de \u00edons H + (pr\u00f3tons) atrav\u00e9s de uma membrana. Este diagn\u00f3stico \u00e9 com defici\u00eancia do Complexo II, que consiste em quatro subunidades de prote\u00ednas: SDHA, SDHB, SDHC e SDHD. Outros doadores de el\u00e9trons (por exemplo, \u00e1cidos graxos e glicerol 3-fosfato) tamb\u00e9m direcionam el\u00e9trons em Q (via FAD)."},"en":{"language":"en","value":"This refers to isolated coupled electron transfer between an electron donor (such as NADH) and an electron acceptor (such as O2) with the transfer of H+ ions (protons) across a membrane. This diagnosis is with deficiency in Complex II, consisting of four protein subunits: SDHA, SDHB, SDHC, and SDHD. Other electron donors (e.g., fatty acids an glycerol 3-phosphate) also direct electrons into Q (via FAD)."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"ca0704114d7f06e74a002f47b63a3cac277a23f4","datavalue":{"value":"https://id.who.int/icd/entity/369066691","type":"string"},"datatype":"url"},"type":"statement","id":"Q102297$99E1E400-B153-4D08-990B-C6E59BDD1678","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"b88fa070d0066429dd4b4a8caffac574e11112f4","datavalue":{"value":"CID11:ID_369066691","type":"string"},"datatype":"string"},"type":"statement","id":"Q102297$F329819A-6298-491D-A314-931596541D0E","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"0ed3851411cf92f83b731160031d8e24c848dafd","datavalue":{"value":"dki-india-ID_369066691","type":"string"},"datatype":"string"},"type":"statement","id":"Q102297$B7F8E975-9C2D-47AE-BA63-D1383967279B","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q102297$3A91E79B-0386-4B4B-B2DC-31F1DFE57216","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q102297$9FD9E3A3-E7B7-455C-A892-8A21D365D0A5","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"378ac503ed43f21e1f461d2823a6ad59da580514","datavalue":{"value":{"time":"+2026-08-15T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q102297$07CC6AD7-EAE1-472A-88E5-2DBD70794E36","rank":"normal"}]},"sitelinks":{}}}}