{"entities":{"Q101021":{"pageid":91414,"ns":120,"title":"Item:Q101021","lastrevid":577244,"modified":"2026-08-16T17:48:39Z","type":"item","id":"Q101021","labels":{"mul":{"language":"mul","value":"ID_1854850844"},"pt-br":{"language":"pt-br","value":"Ganglionopatia sensitiva autoimune, autoanticorpo neuronal negativo"},"en":{"language":"en","value":"Autoimmune sensory ganglionopathy, neural autoantibody negative"}},"descriptions":{"pt-br":{"language":"pt-br","value":"A ganglionopatia sensitiva autoimune ocorre como neuropatia sensorial aguda, em associa\u00e7\u00e3o com a s\u00edndrome de Sj\u00f6gren tamb\u00e9m pansenssitiva, pequenas fibras, CANVAS (Ataxia cerebelar, neuropatia, s\u00edndrome de arreflexia vestibular), condi\u00e7\u00f5es t\u00f3xicas como intoxica\u00e7\u00e3o por piridoxina e tamb\u00e9m tratamento com cisplatina devem ser considerados._x000D_ Tem um in\u00edcio subagudo, perda sensorial grave resultando em ataxia. O in\u00edcio pode ser assim\u00e9trico, geralmente come\u00e7ando nos bra\u00e7os e associado \u00e0 dor neurop\u00e1tica. Uma vez estabelecido, tem curso cr\u00f4nico e ininterrupto, incapacitando o paciente. Anticorpo negativo."},"en":{"language":"en","value":"Autoimmune sensory ganglionopathy occurs as acute sensory neuropathy, in association with Sj\u00f6gren`s syndrome also pansensory, small fibre, CANVAS (Cerebellar Ataxia, neuropathy, vestibular areflexia syndrome, toxic conditions as pyridoxin intoxication and also cis platinum treatment must be considered. It has a subacute onset, severe sensory loss resulting in ataxia. The onset can be asymmetric, often beginning in the arms and associated with neuropathic pain. Once established it has a chronic and unremitting course disabling the patient. Antibody negative."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"1d633b630aa11b4f4c24b53da818d87db21d4be7","datavalue":{"value":"https://id.who.int/icd/entity/1854850844","type":"string"},"datatype":"url"},"type":"statement","id":"Q101021$DCE80DD9-EC73-49F2-AE1A-609B103881D7","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"6ebe06ec2119694e8f0c597f163e74e7e9217aa1","datavalue":{"value":"CID11:ID_1854850844","type":"string"},"datatype":"string"},"type":"statement","id":"Q101021$14716D60-B8FA-4776-AC0E-A64DAA06408A","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"b5b3dad4f1ce58263b9bb79bd8a1b6b6299c48a5","datavalue":{"value":"dki-india-ID_1854850844","type":"string"},"datatype":"string"},"type":"statement","id":"Q101021$9E9BDF7A-727D-448E-89FD-FA6D02547B38","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q101021$E6E3F53F-71C3-432D-B093-3B19C5954B7E","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q101021$B1312342-2D79-42ED-911E-E6E1FA3A8DBB","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"378ac503ed43f21e1f461d2823a6ad59da580514","datavalue":{"value":{"time":"+2026-08-15T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q101021$83604E69-A6BA-4ECE-8470-5EC3BD3015A0","rank":"normal"}]},"sitelinks":{}}}}