{"entities":{"Q100880":{"pageid":91273,"ns":120,"title":"Item:Q100880","lastrevid":576221,"modified":"2026-08-16T17:39:36Z","type":"item","id":"Q100880","labels":{"mul":{"language":"mul","value":"ID_217113223"},"pt-br":{"language":"pt-br","value":"Paraplegia esp\u00e1stica autoss\u00f4mica dominante tipo 10"},"en":{"language":"en","value":"Autosomal dominant spastic paraplegia type 10"}},"descriptions":{"pt-br":{"language":"pt-br","value":"S\u00edndrome de paraplegia esp\u00e1stica autoss\u00f4mica dominante que \u00e9 categorizada como forma pura ou fen\u00f3tipo complexo. A forma pura envolve espasticidade dos membros inferiores, hiperreflexia e respostas extensoras plantares, apresentando-se na inf\u00e2ncia ou adolesc\u00eancia. O fen\u00f3tipo complexo est\u00e1 associado a achados adicionais, como neuropatia perif\u00e9rica com amiotrofia de membros superiores, incapacidade intelectual moderada e parkinsonismo."},"en":{"language":"en","value":"Autosomal dominant spastic paraplegia syndrome that is categorized as either pure form or complex phenotype. The pure form involves lower limb spasticity, hyperreflexia and extensor plantar responses, presenting in childhood or adolescence. The complex phenotype is associated with additional findings such as peripheral neuropathy with upper limb amyotrophy, moderate intellectual disability and parkinsonism."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"3a0ba2f6a119c7c84dce15d49d24f05944ad56de","datavalue":{"value":"https://id.who.int/icd/entity/217113223","type":"string"},"datatype":"url"},"type":"statement","id":"Q100880$096B376D-59C7-44D0-AA7A-BD3B83D4D9F9","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"161f73d537ae816c4458e29c486d1feca59f404a","datavalue":{"value":"CID11:ID_217113223","type":"string"},"datatype":"string"},"type":"statement","id":"Q100880$BFE5C040-E79A-440F-809D-49F103070C79","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"9172f0d85fcbd53b54e3d74d9018fcaa4ab66397","datavalue":{"value":"dki-india-ID_217113223","type":"string"},"datatype":"string"},"type":"statement","id":"Q100880$2981D311-D555-49F8-A41E-E26EAA790F83","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q100880$D1B427C3-15FF-45C0-9E03-29A760FEB493","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q100880$B93CD6FA-4F75-4084-B836-6B4D7846C6A9","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"378ac503ed43f21e1f461d2823a6ad59da580514","datavalue":{"value":{"time":"+2026-08-15T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q100880$F06C2D20-006E-4787-8386-8FF1FF8C2680","rank":"normal"}]},"sitelinks":{}}}}