Doubly committed juxta-arterial ventricular septal defect with posteriorly malaligned fibrous outlet septum and perimembranous extension (Q108288)

A congenital cardiac malformation in which there is an outlet ventricular septal defect with perimembranous extension, bordered superiorly by the area of fibrous continuity or a fibrous outlet septum between the aortic and pulmonary valves, and the fibrous outlet septum is malaligned in a postero-caudal fashion with respect to the trabecular muscular septum such that there is usually obstruction to the left ventricular outflow tract.