Dilated cardiomyopathy due to mucopolysaccharidoses (Q95459)

Dilated cardiomyopathy due to mucopolysaccharidoses is the presence of dilated cardiomyopathy in association with the lysosomal accumulation of glycosaminoglycans (mucopolysaccharides). There are at least 7 main subtypes, with numerous associated mutations, with dilated cardiomyopathy noted in Type I (Hurler syndrome) and Type VI (Maroteaux-Lamy syndrome).