Autosomal recessive agammaglobulinaemia (Q102700)
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Autosomal agammaglobulinemia is a primary immune deficiency characterised by a complete lack of circulating mature B cells, resulting in agammaglobulinemia leading to particular susceptibility to bacterial infections of the respiratory and digestive tracts. Enteroviral meningo-encephalitis is a very severe and not infrequent complication.
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | ID_1395443519 |
||
| English | Autosomal recessive agammaglobulinaemia |
Autosomal agammaglobulinemia is a primary immune deficiency characterised by a complete lack of circulating mature B cells, resulting in agammaglobulinemia leading to particular susceptibility to bacterial infections of the respiratory and digestive tracts. Enteroviral meningo-encephalitis is a very severe and not infrequent complication. |
Statements
CID11:ID_1395443519
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