Apple-peel deformity (Q96760)

Apple peel deformity is one of the most severe variant of jejunal atresia with a high mortality. It is characterised by atresia and wrapping of the distal small intestine in a spiral pattern around a thin vascular pedicle, in which a single branch of the superior mesenteric artery fully develops, supplying, in a retrograde fashion, a markedly shortened ileum, arranged in a radiologic pattern fancifully likened to a reversed ‘Christmas tree’.