Congenital peripheral pulmonary arterial stenosis or hypoplasia at or beyond hilar bifurcation (Q96371)

A congenital cardiovascular malformation of a pulmonary artery, distal to its first branch, in which there is luminal narrowing (below the lower limit of normal adjusted for body size). Additional information: peripheral pulmonary artery narrowing or hypoplasia at or beyond the hilar bifurcation. The stenosis or hypoplasia may be isolated or associated with other cardiovascular lesions.