Von Willebrand disease type 3 (Q84143)
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Type 3 von Willebrand disease is the most severe form of VWD characterised by a bleeding disorder associated with a total or near-total absence of Willebrand factor (von Willebrand factor; VWF) in the plasma and cellular compartments, also leading to a profound deficiency of plasmatic factor VIII (FVIII). The type 3 disease is the rarest form of VWD, accounting for less than 5% of all cases.
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | ID_805917536 |
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| English | Von Willebrand disease type 3 |
Type 3 von Willebrand disease is the most severe form of VWD characterised by a bleeding disorder associated with a total or near-total absence of Willebrand factor (von Willebrand factor; VWF) in the plasma and cellular compartments, also leading to a profound deficiency of plasmatic factor VIII (FVIII). The type 3 disease is the rarest form of VWD, accounting for less than 5% of all cases. |
Statements
CID11:ID_805917536
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