Congenital analbuminaemia (Q107767): Difference between revisions

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A analbuminemia congênita é caracterizada pela ausência ou redução drástica da albumina sérica humana circulante. Os pacientes com analbuminemia congênita apresentam apenas alguns sinais clínicos leves e anormalidades bioquímicas, incluindo fadiga, pressão arterial baixa, edema, concentração aumentada de várias proteínas plasmáticas e meia-vida prolongada da albumina.
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Congenital analbuminaemia is characterised by the absence or dramatic reduction of circulating human serum albumin (HSA). Patients with congenital analbuminaemia present with only a few mild clinical signs and biochemical abnormalities including fatigue, low blood pressure, oedema, increased concentration of several plasma proteins and a prolonged albumin half-life.

Revision as of 14:48, 17 August 2026

Congenital analbuminaemia is characterised by the absence or dramatic reduction of circulating human serum albumin (HSA). Patients with congenital analbuminaemia present with only a few mild clinical signs and biochemical abnormalities including fatigue, low blood pressure, oedema, increased concentration of several plasma proteins and a prolonged albumin half-life.
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    Congenital analbuminaemia
    Congenital analbuminaemia is characterised by the absence or dramatic reduction of circulating human serum albumin (HSA). Patients with congenital analbuminaemia present with only a few mild clinical signs and biochemical abnormalities including fatigue, low blood pressure, oedema, increased concentration of several plasma proteins and a prolonged albumin half-life.

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