Autosomal recessive agammaglobulinaemia (Q102700): Difference between revisions

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Revision as of 19:54, 16 August 2026

Autosomal agammaglobulinemia is a primary immune deficiency characterised by a complete lack of circulating mature B cells, resulting in agammaglobulinemia leading to particular susceptibility to bacterial infections of the respiratory and digestive tracts. Enteroviral meningo-encephalitis is a very severe and not infrequent complication.
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    Autosomal recessive agammaglobulinaemia
    Autosomal agammaglobulinemia is a primary immune deficiency characterised by a complete lack of circulating mature B cells, resulting in agammaglobulinemia leading to particular susceptibility to bacterial infections of the respiratory and digestive tracts. Enteroviral meningo-encephalitis is a very severe and not infrequent complication.

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      CID11:ID_1395443519
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      dki-india-ID_1395443519
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