Autoimmune opsoclonus myoclonus (Q100595): Difference between revisions
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Opsoclônus-mioclônus (OM) autoimune é um transtorno inflamatório imunomediado da movimentação ocular [ver definição de opsoclônus-mioclônus] que não está associado a um câncer subjacente. Pacientes podem ter história pessoal ou familiar de outros transtornos autoimunes. Autoanticorpos neurais concomitantes podem ser encontrados (por exemplo anticorpos ácido glutâmico descarboxilase 65), enquanto autoanticorpos não órgãos específicos também podem sugerir uma pista para uma potencial etiologia autoimune. O rastreamento de câncer para neuroblastoma em crianças e para cânceres de mama e pulmão em adultos é recomendado para excluir OM paraneoplásico. _x000D_ Autoanticorpos associados: _x000D_ GAD65 (anticorpos ácido glutâmico descarboxilase 65). | |||
| description / en | description / en | ||
Autoimmune opsoclonus myoclonus (OM) is an immune mediated inflammatory eye movement disorder [see opsoclonus myoclonus definition] which is not associated with an underlying cancer. Patients may have a personal or family history of other autoimmune disorders. Accompanying neural autoantibodies may be found (e.g. glutamic acid decarboxylase 65 antibodies) while non-organ specific autoantibodies may also give a clue to a potential autoimmune etiology. Cancer screening for neuroblastomas in children and lung and breast cancers in adults is recommended to exclude paraneoplastic OM. Associated autoantibodies: GAD65 (glutamic acid decarboxylase-65 antibodies). | |||
Revision as of 17:19, 16 August 2026
Autoimmune opsoclonus myoclonus (OM) is an immune mediated inflammatory eye movement disorder [see opsoclonus myoclonus definition] which is not associated with an underlying cancer. Patients may have a personal or family history of other autoimmune disorders. Accompanying neural autoantibodies may be found (e.g. glutamic acid decarboxylase 65 antibodies) while non-organ specific autoantibodies may also give a clue to a potential autoimmune etiology. Cancer screening for neuroblastomas in children and lung and breast cancers in adults is recommended to exclude paraneoplastic OM. Associated autoantibodies: GAD65 (glutamic acid decarboxylase-65 antibodies).
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | ID_1316792639 |
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| English | Autoimmune opsoclonus myoclonus |
Autoimmune opsoclonus myoclonus (OM) is an immune mediated inflammatory eye movement disorder [see opsoclonus myoclonus definition] which is not associated with an underlying cancer. Patients may have a personal or family history of other autoimmune disorders. Accompanying neural autoantibodies may be found (e.g. glutamic acid decarboxylase 65 antibodies) while non-organ specific autoantibodies may also give a clue to a potential autoimmune etiology. Cancer screening for neuroblastomas in children and lung and breast cancers in adults is recommended to exclude paraneoplastic OM. Associated autoantibodies: GAD65 (glutamic acid decarboxylase-65 antibodies). |
