Liver cirrhosis in atypical cystic fibrosis (Q100276): Difference between revisions

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É a consequência da doença hepática crônica caracterizada pela substituição do tecido hepático por fibrose, tecido cicatricial e nódulos regenerativos (aglomerados que ocorrem como resultado de um processo no qual o tecido lesado é regenerado), levando à perda da função hepática, em uma doença genética autossômica recessiva atípica que afeta mais criticamente os pulmões, mas também pâncreas, fígado e intestino. Caracteriza-se pelo transporte anormal de cloretos e sódio através de um epitélio, levando à produção de secreções espessas e viscosas.
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This is a consequence of chronic liver disease characterised by replacement of liver tissue by fibrosis, scar tissue and regenerative nodules (lumps that occur as a result of a process in which damaged tissue is regenerated), leading to loss of liver function, in an atypical autosomal recessive genetic disorder that affects most critically the lungs, and also the pancreas, liver, and intestine. It is characterised by abnormal transport of chloride and sodium across an epithelium, leading to thick, viscous secretions.

Revision as of 16:58, 16 August 2026

This is a consequence of chronic liver disease characterised by replacement of liver tissue by fibrosis, scar tissue and regenerative nodules (lumps that occur as a result of a process in which damaged tissue is regenerated), leading to loss of liver function, in an atypical autosomal recessive genetic disorder that affects most critically the lungs, and also the pancreas, liver, and intestine. It is characterised by abnormal transport of chloride and sodium across an epithelium, leading to thick, viscous secretions.
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ID_634798932
    English
    Liver cirrhosis in atypical cystic fibrosis
    This is a consequence of chronic liver disease characterised by replacement of liver tissue by fibrosis, scar tissue and regenerative nodules (lumps that occur as a result of a process in which damaged tissue is regenerated), leading to loss of liver function, in an atypical autosomal recessive genetic disorder that affects most critically the lungs, and also the pancreas, liver, and intestine. It is characterised by abnormal transport of chloride and sodium across an epithelium, leading to thick, viscous secretions.

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