Intestinal epithelial dysplasia (Q100080): Difference between revisions

From determinar.ia.br - Determine suas informações
Changed label, description and/or aliases in pt-br, en
Changed an Item
Property / Canonical URI
 
Property / Canonical URI: https://id.who.int/icd/entity/1536004957 / rank
 
Normal rank

Revision as of 16:46, 16 August 2026

Intestinal epithelial dysplasia, also known as tufting enteropathy, is a congenital enteropathy presenting with early-onset severe intractable diarrhoea sometimes causing irreversible intestinal failure. IED is thought to be related to abnormal enterocytes development and/or differentiation, with specific histological abnormalities involving the epithelium with disorganisation of surface enterocytes with focal crowding, resembling tufts. Several associated specific features were reported, including abnormal deposition of laminin and heparan sulphate proteoglycan (HSPG) in the basement membrane, increased expression of desmoglein and ultrastructural changes in the desmosomes, and abnormal distribution of alpha2beta1 integrin adhesion molecules.
Language Label Description Also known as
default for all languages
ID_1536004957
    English
    Intestinal epithelial dysplasia
    Intestinal epithelial dysplasia, also known as tufting enteropathy, is a congenital enteropathy presenting with early-onset severe intractable diarrhoea sometimes causing irreversible intestinal failure. IED is thought to be related to abnormal enterocytes development and/or differentiation, with specific histological abnormalities involving the epithelium with disorganisation of surface enterocytes with focal crowding, resembling tufts. Several associated specific features were reported, including abnormal deposition of laminin and heparan sulphate proteoglycan (HSPG) in the basement membrane, increased expression of desmoglein and ultrastructural changes in the desmosomes, and abnormal distribution of alpha2beta1 integrin adhesion molecules.

      Statements