Bernard-Soulier syndrome (Q93445): Difference between revisions

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A síndrome de Bernard-Soulier, também conhecida como distrofia trombocítica hemorragípara, é um distúrbio hemorrágico hereditário que afeta a linhagem de megacariócitos/plaquetas e é caracterizada por tendência hemorrágica, plaquetas gigantes no sangue e contagens plaquetárias baixas.
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Bernard-Soulier Syndrome, also known as haemorrhagiparous thrombocytic dystrophy, is a hereditary bleeding disorder affecting the megakaryocyte/platelet lineage and characterised by bleeding tendency, giant blood platelets and low platelet counts.

Revision as of 08:33, 16 August 2026

Bernard-Soulier Syndrome, also known as haemorrhagiparous thrombocytic dystrophy, is a hereditary bleeding disorder affecting the megakaryocyte/platelet lineage and characterised by bleeding tendency, giant blood platelets and low platelet counts.
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    Bernard-Soulier syndrome
    Bernard-Soulier Syndrome, also known as haemorrhagiparous thrombocytic dystrophy, is a hereditary bleeding disorder affecting the megakaryocyte/platelet lineage and characterised by bleeding tendency, giant blood platelets and low platelet counts.

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