Juvenile dermatomyositis with lipodystrophy (Q92505): Difference between revisions
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Revision as of 07:38, 16 August 2026
Juvenile dermatomyositis with lipodystrophy is a chronic systemic autoimmune disease characterised by early-onset proximal weakness and characteristic skin rashes, associated with loss of subcutaneous fat in a localised or generalised distribution, frequently with resultant metabolic abnormalities such as insulin resistance, diabetes and hyperlipidaemia. These patients have a loss of mature, functional adipocytes, as opposed to an absence of lipid in otherwise normal adipocytes.
| Language | Label | Description | Also known as |
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| default for all languages | ID_2133970870 |
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| English | Juvenile dermatomyositis with lipodystrophy |
Juvenile dermatomyositis with lipodystrophy is a chronic systemic autoimmune disease characterised by early-onset proximal weakness and characteristic skin rashes, associated with loss of subcutaneous fat in a localised or generalised distribution, frequently with resultant metabolic abnormalities such as insulin resistance, diabetes and hyperlipidaemia. These patients have a loss of mature, functional adipocytes, as opposed to an absence of lipid in otherwise normal adipocytes. |
