Amyopathic juvenile dermatomyositis (Q92502): Difference between revisions
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Dermatomiosite amiopática de início juvenil é uma variante incomum da dermatomiosite de início juvenil (DMJ), caracterizada pelas clássicas manifestações cutâneas da dermatomiosite por pelo menos 6 meses sem evidência clínica ou laboratorial de doença muscular. Calcinose cutânea, vasculopatia e doença pulmonar intersticial frequentemente complicam o curso da DMJ clássica, mas são infrequentes na DMJ amiopática. Aproximadamente 75% dos pacientes com DMJ amiopática permanecerão livres de doença muscular após anos de acompanhamento, enquanto aproximadamente 25% dos pacientes evoluirão para DMJ clássica. | |||
| description / en | description / en | ||
Juvenile-onset amyopathic dermatomyositis is an uncommon variant of juvenile-onset dermatomyositis (JDM), characterised by the hallmark cutaneous features of dermatomyositis for at least 6 months without clinical or laboratory evidence of muscle disease. Cutaneous calcinosis, vasculopathy, and interstitial lung disease frequently complicate the course of classic JDM, but are infrequent in amyopathic JDM. Approximately 75% of amyopathic JDM patients will remain free from muscle disease after years of follow-up, while approximately 25% of patients will evolve to having classic JDM. | |||
Revision as of 07:38, 16 August 2026
Juvenile-onset amyopathic dermatomyositis is an uncommon variant of juvenile-onset dermatomyositis (JDM), characterised by the hallmark cutaneous features of dermatomyositis for at least 6 months without clinical or laboratory evidence of muscle disease. Cutaneous calcinosis, vasculopathy, and interstitial lung disease frequently complicate the course of classic JDM, but are infrequent in amyopathic JDM. Approximately 75% of amyopathic JDM patients will remain free from muscle disease after years of follow-up, while approximately 25% of patients will evolve to having classic JDM.
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | ID_140962917 |
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| English | Amyopathic juvenile dermatomyositis |
Juvenile-onset amyopathic dermatomyositis is an uncommon variant of juvenile-onset dermatomyositis (JDM), characterised by the hallmark cutaneous features of dermatomyositis for at least 6 months without clinical or laboratory evidence of muscle disease. Cutaneous calcinosis, vasculopathy, and interstitial lung disease frequently complicate the course of classic JDM, but are infrequent in amyopathic JDM. Approximately 75% of amyopathic JDM patients will remain free from muscle disease after years of follow-up, while approximately 25% of patients will evolve to having classic JDM. |
