Autoinflammatory granulomatosis of childhood (Q88714): Difference between revisions
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A artrite granulomatosa da infância designa uma doença inflamatória crônica caracterizada por poliartrite granulomatosa, uveíte e erupção cutânea com início típico antes dos 5 anos de idade. Pode se apresentar de forma familiar, denominada Síndrome de Blau (SB), e de forma esporádica, conhecida como sarcoidose de início precoce. | |||
| description / en | description / en | ||
Granulomatous arthritis of childhood designates a chronic inflammatory disease characterised by granulomatous polyarthritis, uveitis and rash with a typical onset before 5 years. It can present in a familial form, called Blau Syndrome (BS), and a sporadic from, known as early onset sarcoidosis. | |||
Revision as of 15:06, 15 August 2026
Granulomatous arthritis of childhood designates a chronic inflammatory disease characterised by granulomatous polyarthritis, uveitis and rash with a typical onset before 5 years. It can present in a familial form, called Blau Syndrome (BS), and a sporadic from, known as early onset sarcoidosis.
| Language | Label | Description | Also known as |
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| default for all languages | ID_1609700846 |
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| English | Autoinflammatory granulomatosis of childhood |
Granulomatous arthritis of childhood designates a chronic inflammatory disease characterised by granulomatous polyarthritis, uveitis and rash with a typical onset before 5 years. It can present in a familial form, called Blau Syndrome (BS), and a sporadic from, known as early onset sarcoidosis. |
