Rippling muscle disease with myasthenia gravis (Q88660): Difference between revisions

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A doença de músculo rippling imunomediada (DMRi) pode ocorrer concomitantemente com Miastenia Gravis (MG) positiva para receptor de acetilcolina sem mutações no gene da caveolina-3 da linha germinativa. Os inibidores da acetilcolinesterase podem agravar os sintomas. MG generalizada e DMRi são tratáveis com drogas imunomoduladoras e imunossupressoras, como prednisona ou azatioprina com alívio oportuno e duradouro.
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Immune-mediated rippling muscle disease (iRMD) may concomitantly occur with Acetylcholine receptor positive Myasthenia Gravis (MG) without germline caveolin-3 gene mutations. Acetylcholinesterase-inhibitors may aggravate the symptoms. generalised MG and iRMD are treatable by immunomodulating and immunosuppressant drugs such as prednisone or azathioprine with timely and enduring relief.

Revision as of 15:00, 15 August 2026

Immune-mediated rippling muscle disease (iRMD) may concomitantly occur with Acetylcholine receptor positive Myasthenia Gravis (MG) without germline caveolin-3 gene mutations. Acetylcholinesterase-inhibitors may aggravate the symptoms. generalised MG and iRMD are treatable by immunomodulating and immunosuppressant drugs such as prednisone or azathioprine with timely and enduring relief.
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    Rippling muscle disease with myasthenia gravis
    Immune-mediated rippling muscle disease (iRMD) may concomitantly occur with Acetylcholine receptor positive Myasthenia Gravis (MG) without germline caveolin-3 gene mutations. Acetylcholinesterase-inhibitors may aggravate the symptoms. generalised MG and iRMD are treatable by immunomodulating and immunosuppressant drugs such as prednisone or azathioprine with timely and enduring relief.

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