Rippling muscle disease with myasthenia gravis (Q88660): Difference between revisions
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A doença de músculo rippling imunomediada (DMRi) pode ocorrer concomitantemente com Miastenia Gravis (MG) positiva para receptor de acetilcolina sem mutações no gene da caveolina-3 da linha germinativa. Os inibidores da acetilcolinesterase podem agravar os sintomas. MG generalizada e DMRi são tratáveis com drogas imunomoduladoras e imunossupressoras, como prednisona ou azatioprina com alívio oportuno e duradouro. | |||
| description / en | description / en | ||
Immune-mediated rippling muscle disease (iRMD) may concomitantly occur with Acetylcholine receptor positive Myasthenia Gravis (MG) without germline caveolin-3 gene mutations. Acetylcholinesterase-inhibitors may aggravate the symptoms. generalised MG and iRMD are treatable by immunomodulating and immunosuppressant drugs such as prednisone or azathioprine with timely and enduring relief. | |||
Revision as of 15:00, 15 August 2026
Immune-mediated rippling muscle disease (iRMD) may concomitantly occur with Acetylcholine receptor positive Myasthenia Gravis (MG) without germline caveolin-3 gene mutations. Acetylcholinesterase-inhibitors may aggravate the symptoms. generalised MG and iRMD are treatable by immunomodulating and immunosuppressant drugs such as prednisone or azathioprine with timely and enduring relief.
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | ID_327350590 |
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| English | Rippling muscle disease with myasthenia gravis |
Immune-mediated rippling muscle disease (iRMD) may concomitantly occur with Acetylcholine receptor positive Myasthenia Gravis (MG) without germline caveolin-3 gene mutations. Acetylcholinesterase-inhibitors may aggravate the symptoms. generalised MG and iRMD are treatable by immunomodulating and immunosuppressant drugs such as prednisone or azathioprine with timely and enduring relief. |
