Caroli disease (Q87266): Difference between revisions
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A doença de Caroli é um transtorno congênito raro caracterizado por dilatação segmentar multifocal dos grandes ductos biliares intra-hepáticos. Ela se apresenta com colangite bacteriana recorrente, cálculos biliares que causam cólica biliar ou episódios de pancreatite. A variante mais comum dessa doença, denominada síndrome de Caroli, é caracterizada por dilatações de grandes ductos biliares associadas à fibrose hepática congênita, com sinais e sintomas de hipertensão portal ou colangite bacteriana. | |||
| description / en | description / en | ||
Caroli's disease is a rare congenital disorder characterised by multifocal, segmental dilatation of the large intrahepatic bile ducts. It presents with recurrent bacterial cholangitis, biliary stones causing biliary pain or episodes of pancreatitis. The more common variant of this disease, named Caroli's syndrome, is characterised by dilatations of the large bile duct associated with congenital hepatic fibrosis, with signs and symptoms of portal hypertension or bacterial cholangitis. | |||
Revision as of 12:49, 15 August 2026
Caroli's disease is a rare congenital disorder characterised by multifocal, segmental dilatation of the large intrahepatic bile ducts. It presents with recurrent bacterial cholangitis, biliary stones causing biliary pain or episodes of pancreatitis. The more common variant of this disease, named Caroli's syndrome, is characterised by dilatations of the large bile duct associated with congenital hepatic fibrosis, with signs and symptoms of portal hypertension or bacterial cholangitis.
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | ID_1757434239 |
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| English | Caroli disease |
Caroli's disease is a rare congenital disorder characterised by multifocal, segmental dilatation of the large intrahepatic bile ducts. It presents with recurrent bacterial cholangitis, biliary stones causing biliary pain or episodes of pancreatitis. The more common variant of this disease, named Caroli's syndrome, is characterised by dilatations of the large bile duct associated with congenital hepatic fibrosis, with signs and symptoms of portal hypertension or bacterial cholangitis. |
