Von Willebrand disease type 3 (Q84143): Difference between revisions
From determinar.ia.br - Determine suas informações
Changed label, description and/or aliases in pt-br, en |
Changed an Item |
||
| Property / Canonical URI | |||
| Property / Canonical URI: https://id.who.int/icd/entity/805917536 / rank | |||
Normal rank | |||
Revision as of 09:30, 15 August 2026
Type 3 von Willebrand disease is the most severe form of VWD characterised by a bleeding disorder associated with a total or near-total absence of Willebrand factor (von Willebrand factor; VWF) in the plasma and cellular compartments, also leading to a profound deficiency of plasmatic factor VIII (FVIII). The type 3 disease is the rarest form of VWD, accounting for less than 5% of all cases.
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | ID_805917536 |
||
| English | Von Willebrand disease type 3 |
Type 3 von Willebrand disease is the most severe form of VWD characterised by a bleeding disorder associated with a total or near-total absence of Willebrand factor (von Willebrand factor; VWF) in the plasma and cellular compartments, also leading to a profound deficiency of plasmatic factor VIII (FVIII). The type 3 disease is the rarest form of VWD, accounting for less than 5% of all cases. |
