Hereditary factor XIII deficiency (Q63970): Difference between revisions

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Deficiência congênita do fator XIII é um transtorno hemorrágico hereditário devido à redução dos níveis e da atividade do fator XIII e caracterizado por diátese hemorrágica frequentemente associada a abortamentos e defeitos na cicatrização de feridas. A deficiência do fator XIII é uma das deficiências mais raras de fator da coagulação. Ambos os sexos são igualmente afetados.
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Congenital factor XIII deficiency is an inherited bleeding disorder due to reduced levels and activity of factor XIII and characterised by haemorrhagic diathesis frequently associated with spontaneous abortions and defective wound healing. Factor XIII deficiency is one of the most rare coagulation factor deficiencies. Both sexes are equally affected.

Revision as of 11:28, 14 August 2026

Congenital factor XIII deficiency is an inherited bleeding disorder due to reduced levels and activity of factor XIII and characterised by haemorrhagic diathesis frequently associated with spontaneous abortions and defective wound healing. Factor XIII deficiency is one of the most rare coagulation factor deficiencies. Both sexes are equally affected.
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ID_2079957863
    English
    Hereditary factor XIII deficiency
    Congenital factor XIII deficiency is an inherited bleeding disorder due to reduced levels and activity of factor XIII and characterised by haemorrhagic diathesis frequently associated with spontaneous abortions and defective wound healing. Factor XIII deficiency is one of the most rare coagulation factor deficiencies. Both sexes are equally affected.

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