Diffuse eosinophilic fasciitis (Q44399): Difference between revisions
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Também chamada de doença de Shulman/fasciíte difusa, a fasciíte eosinofílica difusa é um transtorno idiopático raro associado a endurecimento da pele (sinal da casca de laranja) que geralmente se desenvolve rapidamente. É uma esclerose dérmica e hipodérmica associada a espessamento fibrótico dos septos lobulares adiposos subcutâneos, fáscia superficial e perimísio. Biópsia excisional de espessura total de lesões cutâneas revelando fibrose da fáscia subcutânea é geralmente necessária para o diagnóstico. O início ocorre após esforço físico incomum e traumatismo, especialmente em homens. | |||
| description / en | description / en | ||
Also called Shulman disease/diffuse fasciitis, diffuse eosinophilic fasciitis is a rare idiopathic disorder associated with induration of the skin (orange-peel sign) that generally develops rapidly. It is a dermal and hypodermal sclerosis associated with fibrotic thickening of the subcutaneous adipose lobular septa, superficial fascia, and perimysium. Full thickness excisional biopsy of skin lesions revealing fibrosis of the subcutaneous fascia is generally required for diagnosis. Onset follows unusual physical exertion and trauma, especially in males. | |||
Revision as of 11:51, 13 August 2026
Also called Shulman disease/diffuse fasciitis, diffuse eosinophilic fasciitis is a rare idiopathic disorder associated with induration of the skin (orange-peel sign) that generally develops rapidly. It is a dermal and hypodermal sclerosis associated with fibrotic thickening of the subcutaneous adipose lobular septa, superficial fascia, and perimysium. Full thickness excisional biopsy of skin lesions revealing fibrosis of the subcutaneous fascia is generally required for diagnosis. Onset follows unusual physical exertion and trauma, especially in males.
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | 4A43.4 |
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| English | Diffuse eosinophilic fasciitis |
Also called Shulman disease/diffuse fasciitis, diffuse eosinophilic fasciitis is a rare idiopathic disorder associated with induration of the skin (orange-peel sign) that generally develops rapidly. It is a dermal and hypodermal sclerosis associated with fibrotic thickening of the subcutaneous adipose lobular septa, superficial fascia, and perimysium. Full thickness excisional biopsy of skin lesions revealing fibrosis of the subcutaneous fascia is generally required for diagnosis. Onset follows unusual physical exertion and trauma, especially in males. |
