Polymyositis (Q44384): Difference between revisions
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Polimiosite é uma doença muscular inflamatória de etiologia desconhecida que ocorre predominantemente em adultos, e caracterizada clinicamente por fraqueza muscular proximal (ombros, braços, coxas), muitas vezes com mialgia associada. O envolvimento de músculos faríngeos e esofágicos pode resultar em disfagia e risco de pneumonia por aspiração. Miocardite com distúrbios do ritmo ou cardiomiopatia são uma complicação rara, mas grave. A polimiosite pode estar associada a outras doenças autoimunes, malignidade ou infecção viral. Embora as concentrações séricas de enzimas musculares e a eletromiografia sejam geralmente anormais, o diagnóstico definitivo requer a demonstração de alterações histológicas características, incluindo necrose muscular, regeneração de fibras musculares e infiltração difusa por linfócitos T CD8+, na biópsia muscular. | |||
| description / en | description / en | ||
Polymyositis is an inflammatory muscle disease of unknown aetiology occurring predominantly in adults and characterised clinically by proximal muscle weakness (shoulders, arms, thighs), often with associated myalgia. Involvement of pharyngeal and oesophageal muscles may result in dysphagia and a risk of aspiration pneumonia. Myocarditis with rhythm disturbances or cardiomyopathy is a rare but serious complication. Polymyositis may be associated with other autoimmune diseases, malignancy or viral infection. Although serum muscle enzyme concentrations and electromyography are usually abnormal, definitive diagnosis requires demonstration of characteristic histological changes, including muscle necrosis, muscle fibre regeneration and diffuse infiltration by CD8+ T lymphocytes, on muscle biopsy. | |||
Revision as of 11:49, 13 August 2026
Polymyositis is an inflammatory muscle disease of unknown aetiology occurring predominantly in adults and characterised clinically by proximal muscle weakness (shoulders, arms, thighs), often with associated myalgia. Involvement of pharyngeal and oesophageal muscles may result in dysphagia and a risk of aspiration pneumonia. Myocarditis with rhythm disturbances or cardiomyopathy is a rare but serious complication. Polymyositis may be associated with other autoimmune diseases, malignancy or viral infection. Although serum muscle enzyme concentrations and electromyography are usually abnormal, definitive diagnosis requires demonstration of characteristic histological changes, including muscle necrosis, muscle fibre regeneration and diffuse infiltration by CD8+ T lymphocytes, on muscle biopsy.
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | 4A41.1 |
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| English | Polymyositis |
Polymyositis is an inflammatory muscle disease of unknown aetiology occurring predominantly in adults and characterised clinically by proximal muscle weakness (shoulders, arms, thighs), often with associated myalgia. Involvement of pharyngeal and oesophageal muscles may result in dysphagia and a risk of aspiration pneumonia. Myocarditis with rhythm disturbances or cardiomyopathy is a rare but serious complication. Polymyositis may be associated with other autoimmune diseases, malignancy or viral infection. Although serum muscle enzyme concentrations and electromyography are usually abnormal, definitive diagnosis requires demonstration of characteristic histological changes, including muscle necrosis, muscle fibre regeneration and diffuse infiltration by CD8+ T lymphocytes, on muscle biopsy. |
