Juvenile polymyositis (Q44382): Difference between revisions

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A polimiosite juvenil é uma rara miopatia inflamatória idiopática da infância. É frequentemente diagnosticada erroneamente, pois não possui um fenótipo clínico único. Tradicionalmente, apresenta-se com fraqueza dos músculos proximais que evolui ao longo de semanas a meses. As características histológicas primárias são a variabilidade do tamanho das fibras, fibras necróticas e em regeneração dispersas e infiltrados celulares perivasculares e no endomísio.
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Juvenile polymyositis is a rare childhood idiopathic inflammatory myopathy. It is frequently misdiagnosed, as it lacks a unique clinical phenotype. Traditionally, it presents with weakness of the proximal muscles that evolves over weeks to months. The primary histologic features are fibre size variability, scattered necrotic and regenerating fibres, and perivascular and endomysial cellular infiltrates.

Revision as of 11:49, 13 August 2026

Juvenile polymyositis is a rare childhood idiopathic inflammatory myopathy. It is frequently misdiagnosed, as it lacks a unique clinical phenotype. Traditionally, it presents with weakness of the proximal muscles that evolves over weeks to months. The primary histologic features are fibre size variability, scattered necrotic and regenerating fibres, and perivascular and endomysial cellular infiltrates.
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4A41.10
    English
    Juvenile polymyositis
    Juvenile polymyositis is a rare childhood idiopathic inflammatory myopathy. It is frequently misdiagnosed, as it lacks a unique clinical phenotype. Traditionally, it presents with weakness of the proximal muscles that evolves over weeks to months. The primary histologic features are fibre size variability, scattered necrotic and regenerating fibres, and perivascular and endomysial cellular infiltrates.

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