Retroperitoneal fibrosis (Q43558): Difference between revisions
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Fibrose retroperitoneal (FRP) é uma doença caracterizada pela formação de extensa proliferação de tecido fibroso no retroperitônio, resultando em encarceramento e obstrução de estruturas retroperitoneais, particularmente os ureteres. A FRP pode ser classificada em primária (idiopática), o que significa que sua causa não é conhecida, ou secundária. No entanto, sua associação com várias condições imunomediadas e sua resposta ao tratamento imunossupressor têm levado á especulação de etiologia autoimune para a FRP idiopática. Um terço dos casos são secundários a neoplasias malignas, medicamentos, traumatismo e algumas infecções. | |||
| description / en | description / en | ||
Retroperitoneal fibrosis (RPF) is a disease characterised by the development of extensive proliferation of fibrous tissue in the retroperitoneum, resulting in entrapment and obstruction of retroperitoneal structures, notably the ureters. RPF can be classified as primary (idiopathic) meaning that the cause is not known or secondary. But its association with various immune-related conditions and response to immunosuppression have led to speculation regarding an autoimmune aetiology of idiopathic RPF. One-third of the cases are secondary to malignancy, medication, trauma, or certain infections. | |||
Revision as of 10:37, 13 August 2026
Retroperitoneal fibrosis (RPF) is a disease characterised by the development of extensive proliferation of fibrous tissue in the retroperitoneum, resulting in entrapment and obstruction of retroperitoneal structures, notably the ureters. RPF can be classified as primary (idiopathic) meaning that the cause is not known or secondary. But its association with various immune-related conditions and response to immunosuppression have led to speculation regarding an autoimmune aetiology of idiopathic RPF. One-third of the cases are secondary to malignancy, medication, trauma, or certain infections.
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | FB51.4 |
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| English | Retroperitoneal fibrosis |
Retroperitoneal fibrosis (RPF) is a disease characterised by the development of extensive proliferation of fibrous tissue in the retroperitoneum, resulting in entrapment and obstruction of retroperitoneal structures, notably the ureters. RPF can be classified as primary (idiopathic) meaning that the cause is not known or secondary. But its association with various immune-related conditions and response to immunosuppression have led to speculation regarding an autoimmune aetiology of idiopathic RPF. One-third of the cases are secondary to malignancy, medication, trauma, or certain infections. |
