Catecholaminergic polymorphic ventricular tachycardia (Q42400): Difference between revisions
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Taquicardia ventricular polimórfica catecolaminérgica (TVPC) é um grave distúrbio arritmogênico genético da infância caracterizado por taquicardia ventricular induzida por adrenalina (taquicardia ventricular bidirecional e, menos frequentemente, taquicardia supraventricular e fibrilação atrial) manifestando-se como síncope e morte súbita. | |||
| description / en | description / en | ||
Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a severe genetic arrhythmogenic disorder of childhood characterised by adrenergically-induced ventricular tachycardia (bidirectional ventricular tachycardia and, less frequently, supraventricular tachycardia and atrial fibrillation) manifesting as syncope and sudden death. | |||
Revision as of 08:54, 13 August 2026
Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a severe genetic arrhythmogenic disorder of childhood characterised by adrenergically-induced ventricular tachycardia (bidirectional ventricular tachycardia and, less frequently, supraventricular tachycardia and atrial fibrillation) manifesting as syncope and sudden death.
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | BC65.5 |
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| English | Catecholaminergic polymorphic ventricular tachycardia |
Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a severe genetic arrhythmogenic disorder of childhood characterised by adrenergically-induced ventricular tachycardia (bidirectional ventricular tachycardia and, less frequently, supraventricular tachycardia and atrial fibrillation) manifesting as syncope and sudden death. |
