Demyelination due to systemic vasculitis (Q41134): Difference between revisions
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A vasculatura do SNC pode ser alvo de vasculite sistêmica e inclui as seguitets condições: _x000D_ Vasculite de vasos pequenos-médios: granulomatose de Wegener, poliangeíte microscópica, síndrome de Churg-Strauss, vasculite crioglobulinêmica e doença de Behçet._x000D_ _x000D_ Vasculite de vasos médios: Poliarterite nodosa_x000D_ _x000D_ Vasculite de vasos grandes: arterite de células gigantes, arterite de Takayasu (complicações neurológicas são principalmente devidas a envolvimento de vasos extra-cranianos)._x000D_ _x000D_ Usualmente o envolvimento de SNC coexiste com outras manifestações sistêmicas claramente aparentes, porém alguns pacientes podem apresentar primariamente sintomas proeminentes de disfunção do SNC. | |||
| description / en | description / en | ||
The CNS vasculature can be targeted by systemic vasculitis and include the following conditions; Small-Medium Vessel Vasculitis - Wegener’s granulomatosis, microscopic polyangiitis, Churg-Strauss syndrome, Cryoglobulinemic vasculitis and Behçet’s disease. Medium Vessel Vasculitis - Polyarteritis nodosa Large Vessel Vasculitis - Giant-cell arteritis, Takayasu’s arteritis (Neurologic complications are mainly due to involvement of extracranial vessels). Usually CNS involvement coexists with other clearly apparent systemic manifestations but some patients may present primarily with prominent symptoms of CNS dysfunction | |||
Revision as of 07:12, 13 August 2026
The CNS vasculature can be targeted by systemic vasculitis and include the following conditions; Small-Medium Vessel Vasculitis - Wegener’s granulomatosis, microscopic polyangiitis, Churg-Strauss syndrome, Cryoglobulinemic vasculitis and Behçet’s disease. Medium Vessel Vasculitis - Polyarteritis nodosa Large Vessel Vasculitis - Giant-cell arteritis, Takayasu’s arteritis (Neurologic complications are mainly due to involvement of extracranial vessels). Usually CNS involvement coexists with other clearly apparent systemic manifestations but some patients may present primarily with prominent symptoms of CNS dysfunction
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | 8A45.44 |
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| English | Demyelination due to systemic vasculitis |
The CNS vasculature can be targeted by systemic vasculitis and include the following conditions; Small-Medium Vessel Vasculitis - Wegener’s granulomatosis, microscopic polyangiitis, Churg-Strauss syndrome, Cryoglobulinemic vasculitis and Behçet’s disease. Medium Vessel Vasculitis - Polyarteritis nodosa Large Vessel Vasculitis - Giant-cell arteritis, Takayasu’s arteritis (Neurologic complications are mainly due to involvement of extracranial vessels). Usually CNS involvement coexists with other clearly apparent systemic manifestations but some patients may present primarily with prominent symptoms of CNS dysfunction |
