Amyloidosis (Q40138): Difference between revisions
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A amiloidose é um vasto grupo de doenças definidas pela presença de depósitos de proteínas insolúveis nos tecidos. Seu diagnóstico é baseado em achados histológicos. As amiloidoses são classificadas de acordo com os sinais clínicos e o tipo bioquímico da proteína amilóide envolvida. A maioria das amiloidoses é multissistêmica, 'generalizada' ou 'difusa'. Existem algumas formas de amilose localizada. As formas mais frequentes são amiloidose AL (imunoglobulinas), AA (inflamatória) e ATTR (acúmulo de transtirretina). | |||
| description / en | description / en | ||
Amyloidosis is a vast group of diseases defined by the presence of insoluble protein deposits in tissues. Its diagnosis is based on histological findings. Amyloidoses are classified according to clinical signs and biochemical type of amyloid protein involved. Most amyloidoses are multisystemic, 'generalised' or 'diffuse'. There are a few forms of localised amylosis. The most frequent forms are AL amyloidosis (immunoglobulins), AA (inflammatory), and ATTR (transthyretin accumulation). | |||
Revision as of 05:49, 13 August 2026
Amyloidosis is a vast group of diseases defined by the presence of insoluble protein deposits in tissues. Its diagnosis is based on histological findings. Amyloidoses are classified according to clinical signs and biochemical type of amyloid protein involved. Most amyloidoses are multisystemic, 'generalised' or 'diffuse'. There are a few forms of localised amylosis. The most frequent forms are AL amyloidosis (immunoglobulins), AA (inflammatory), and ATTR (transthyretin accumulation).
| Language | Label | Description | Also known as |
|---|---|---|---|
| default for all languages | 5D00 |
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| English | Amyloidosis |
Amyloidosis is a vast group of diseases defined by the presence of insoluble protein deposits in tissues. Its diagnosis is based on histological findings. Amyloidoses are classified according to clinical signs and biochemical type of amyloid protein involved. Most amyloidoses are multisystemic, 'generalised' or 'diffuse'. There are a few forms of localised amylosis. The most frequent forms are AL amyloidosis (immunoglobulins), AA (inflammatory), and ATTR (transthyretin accumulation). |
